DRAFT

ICD-10-CM/PCS MS-DRG v41.0 Definitions Manual

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Appendix C: Principal diagnoses which convert CC/MCC to non-CC
Page 1366 of 1375
PDX Collection 6991 (continued)
E7210Disorders of sulfur-bearing amino-acid metabolism, unspecified
E7211Homocystinuria
E7212Methylenetetrahydrofolate reductase deficiency
E7219Other disorders of sulfur-bearing amino-acid metabolism
E7220Disorder of urea cycle metabolism, unspecified
E7221Argininemia
E7222Arginosuccinic aciduria
E7223Citrullinemia
E7229Other disorders of urea cycle metabolism
E723Disorders of lysine and hydroxylysine metabolism
E724Disorders of ornithine metabolism
E7250Disorder of glycine metabolism, unspecified
E7251Non-ketotic hyperglycinemia
E7252Trimethylaminuria
E7253Primary hyperoxaluria
E7259Other disorders of glycine metabolism
E7281Disorders of gamma aminobutyric acid metabolism
E7289Other specified disorders of amino-acid metabolism
E729Disorder of amino-acid metabolism, unspecified
E730Congenital lactase deficiency
E731Secondary lactase deficiency
E738Other lactose intolerance
E739Lactose intolerance, unspecified
E7400Glycogen storage disease, unspecified
E7401von Gierke disease
E7402Pompe disease
E7403Cori disease
E7404McArdle disease
E7405Lysosome-associated membrane protein 2 [LAMP2] deficiency
E7409Other glycogen storage disease
E7410Disorder of fructose metabolism, unspecified
E7411Essential fructosuria
E7412Hereditary fructose intolerance
E7419Other disorders of fructose metabolism
E7420Disorders of galactose metabolism, unspecified
E7421Galactosemia
E7429Other disorders of galactose metabolism
E7431Sucrase-isomaltase deficiency
E7439Other disorders of intestinal carbohydrate absorption
E744Disorders of pyruvate metabolism and gluconeogenesis
E74810Glucose transporter protein type 1 deficiency
E74818Other disorders of glucose transport
E74819Disorders of glucose transport, unspecified
E7489Other specified disorders of carbohydrate metabolism
E749Disorder of carbohydrate metabolism, unspecified
E7521Fabry (-Anderson) disease
E7522Gaucher disease
E75240Niemann-Pick disease type A
E75241Niemann-Pick disease type B
E75242Niemann-Pick disease type C
E75243Niemann-Pick disease type D
E75248Other Niemann-Pick disease
E75249Niemann-Pick disease, unspecified
E753Sphingolipidosis, unspecified
E755Other lipid storage disorders
E756Lipid storage disorder, unspecified
E770Defects in post-translational modification of lysosomal enzymes
E771Defects in glycoprotein degradation
E778Other disorders of glycoprotein metabolism
E779Disorder of glycoprotein metabolism, unspecified
E7800Pure hypercholesterolemia, unspecified
E7801Familial hypercholesterolemia
E781Pure hyperglyceridemia
E782Mixed hyperlipidemia
E783Hyperchylomicronemia
E7841Elevated Lipoprotein(a)
E7849Other hyperlipidemia
E785Hyperlipidemia, unspecified
E786Lipoprotein deficiency
E7870Disorder of bile acid and cholesterol metabolism, unspecified
E7879Other disorders of bile acid and cholesterol metabolism
E7881Lipoid dermatoarthritis
E7889Other lipoprotein metabolism disorders
E789Disorder of lipoprotein metabolism, unspecified
E8802Plasminogen deficiency
E8809Other disorders of plasma-protein metabolism, not elsewhere classified
E881Lipodystrophy, not elsewhere classified
E882Lipomatosis, not elsewhere classified
E88811Insulin resistance syndrome, Type A
E88818Other insulin resistance
E88819Insulin resistance, unspecified
E8889Other specified metabolic disorders
 
PDX Collection 6992
C880Waldenstrom macroglobulinemia
D472Monoclonal gammopathy
D890Polyclonal hypergammaglobulinemia
D891Cryoglobulinemia
E700Classical phenylketonuria
E701Other hyperphenylalaninemias
E7020Disorder of tyrosine metabolism, unspecified
E7021Tyrosinemia
E7029Other disorders of tyrosine metabolism
E7030Albinism, unspecified
E70310X-linked ocular albinism
E70311Autosomal recessive ocular albinism
E70318Other ocular albinism
E70319Ocular albinism, unspecified
E70320Tyrosinase negative oculocutaneous albinism
E70321Tyrosinase positive oculocutaneous albinism
E70328Other oculocutaneous albinism
E70329Oculocutaneous albinism, unspecified
E70330Chediak-Higashi syndrome
E70331Hermansky-Pudlak syndrome
E70338Other albinism with hematologic abnormality
E70339Albinism with hematologic abnormality, unspecified
E7039Other specified albinism
E7040Disorders of histidine metabolism, unspecified
E7041Histidinemia
E7049Other disorders of histidine metabolism
E705Disorders of tryptophan metabolism
E7081Aromatic L-amino acid decarboxylase deficiency
E7089Other disorders of aromatic amino-acid metabolism
E709Disorder of aromatic amino-acid metabolism, unspecified
E710Maple-syrup-urine disease
E71110Isovaleric acidemia
E711113-methylglutaconic aciduria
E71118Other branched-chain organic acidurias
E71120Methylmalonic acidemia
E71121Propionic acidemia
E71128Other disorders of propionate metabolism
E7119Other disorders of branched-chain amino-acid metabolism
E712Disorder of branched-chain amino-acid metabolism, unspecified
E7130Disorder of fatty-acid metabolism, unspecified
E7200Disorders of amino-acid transport, unspecified
E7201Cystinuria
E7202Hartnup's disease
E7204Cystinosis
E7209Other disorders of amino-acid transport
E7210Disorders of sulfur-bearing amino-acid metabolism, unspecified
E7211Homocystinuria
E7212Methylenetetrahydrofolate reductase deficiency
E7219Other disorders of sulfur-bearing amino-acid metabolism
E7220Disorder of urea cycle metabolism, unspecified
E7221Argininemia
E7222Arginosuccinic aciduria
E7223Citrullinemia
E7229Other disorders of urea cycle metabolism
E723Disorders of lysine and hydroxylysine metabolism
E724Disorders of ornithine metabolism
E7250Disorder of glycine metabolism, unspecified
E7251Non-ketotic hyperglycinemia
E7252Trimethylaminuria
E7253Primary hyperoxaluria
E7259Other disorders of glycine metabolism
E7281Disorders of gamma aminobutyric acid metabolism
E7289Other specified disorders of amino-acid metabolism
E729Disorder of amino-acid metabolism, unspecified
E730Congenital lactase deficiency
E731Secondary lactase deficiency
E738Other lactose intolerance
E739Lactose intolerance, unspecified
E7400Glycogen storage disease, unspecified
E7401von Gierke disease
E7402Pompe disease
E7403Cori disease
E7404McArdle disease
E7405Lysosome-associated membrane protein 2 [LAMP2] deficiency
E7409Other glycogen storage disease
E7410Disorder of fructose metabolism, unspecified
E7411Essential fructosuria
E7412Hereditary fructose intolerance
E7419Other disorders of fructose metabolism
E7420Disorders of galactose metabolism, unspecified
E7421Galactosemia
E7429Other disorders of galactose metabolism
E7431Sucrase-isomaltase deficiency
E7439Other disorders of intestinal carbohydrate absorption
E744Disorders of pyruvate metabolism and gluconeogenesis
E74810Glucose transporter protein type 1 deficiency
E74818Other disorders of glucose transport
E74819Disorders of glucose transport, unspecified
E7489Other specified disorders of carbohydrate metabolism
E749Disorder of carbohydrate metabolism, unspecified
E7521Fabry (-Anderson) disease
E7522Gaucher disease
E75240Niemann-Pick disease type A
E75241Niemann-Pick disease type B
E75242Niemann-Pick disease type C
E75243Niemann-Pick disease type D
E75248Other Niemann-Pick disease
E75249Niemann-Pick disease, unspecified
E753Sphingolipidosis, unspecified
E755Other lipid storage disorders
E756Lipid storage disorder, unspecified
E770Defects in post-translational modification of lysosomal enzymes
E771Defects in glycoprotein degradation
E778Other disorders of glycoprotein metabolism
E779Disorder of glycoprotein metabolism, unspecified
E7800Pure hypercholesterolemia, unspecified
E7801Familial hypercholesterolemia
E781Pure hyperglyceridemia
E782Mixed hyperlipidemia
E783Hyperchylomicronemia
E7841Elevated Lipoprotein(a)
E7849Other hyperlipidemia
E785Hyperlipidemia, unspecified
E786Lipoprotein deficiency
E7870Disorder of bile acid and cholesterol metabolism, unspecified
E7879Other disorders of bile acid and cholesterol metabolism
E7881Lipoid dermatoarthritis
E7889Other lipoprotein metabolism disorders
E789Disorder of lipoprotein metabolism, unspecified
E8802Plasminogen deficiency
E8809Other disorders of plasma-protein metabolism, not elsewhere classified
E881Lipodystrophy, not elsewhere classified
E882Lipomatosis, not elsewhere classified
E88811Insulin resistance syndrome, Type A
E88818Other insulin resistance
E88819Insulin resistance, unspecified
E8889Other specified metabolic disorders
 
PDX Collection 6993
N000Acute nephritic syndrome with minor glomerular abnormality
N001Acute nephritic syndrome with focal and segmental glomerular lesions
N002Acute nephritic syndrome with diffuse membranous glomerulonephritis
N003Acute nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
N004Acute nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
N005Acute nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
N006Acute nephritic syndrome with dense deposit disease
N007Acute nephritic syndrome with diffuse crescentic glomerulonephritis
N008Acute nephritic syndrome with other morphologic changes
N009Acute nephritic syndrome with unspecified morphologic changes
N00AAcute nephritic syndrome with C3 glomerulonephritis
N010Rapidly progressive nephritic syndrome with minor glomerular abnormality
N011Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions
N012Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis
N013Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
N014Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
N015Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
N016Rapidly progressive nephritic syndrome with dense deposit disease
N017Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis
N018Rapidly progressive nephritic syndrome with other morphologic changes
N019Rapidly progressive nephritic syndrome with unspecified morphologic changes
N01ARapidly progressive nephritic syndrome with C3 glomerulonephritis
N020Recurrent and persistent hematuria with minor glomerular abnormality
N021Recurrent and persistent hematuria with focal and segmental glomerular lesions
N022Recurrent and persistent hematuria with diffuse membranous glomerulonephritis
N023Recurrent and persistent hematuria with diffuse mesangial proliferative glomerulonephritis
N024Recurrent and persistent hematuria with diffuse endocapillary proliferative glomerulonephritis
N025Recurrent and persistent hematuria with diffuse mesangiocapillary glomerulonephritis
N026Recurrent and persistent hematuria with dense deposit disease
N027Recurrent and persistent hematuria with diffuse crescentic glomerulonephritis
N028Recurrent and persistent hematuria with other morphologic changes
N029Recurrent and persistent hematuria with unspecified morphologic changes
N02ARecurrent and persistent hematuria with C3 glomerulonephritis
N02B1Recurrent and persistent immunoglobulin A nephropathy with glomerular lesion
N02B2Recurrent and persistent immunoglobulin A nephropathy with focal and segmental glomerular lesion
N02B3Recurrent and persistent immunoglobulin A nephropathy with diffuse membranoproliferative glomerulonephritis
N02B4Recurrent and persistent immunoglobulin A nephropathy with diffuse membranous glomerulonephritis
N02B5Recurrent and persistent immunoglobulin A nephropathy with diffuse mesangial proliferative glomerulonephritis
N02B6Recurrent and persistent immunoglobulin A nephropathy with diffuse mesangiocapillary glomerulonephritis
N02B9Other recurrent and persistent immunoglobulin A nephropathy
N030Chronic nephritic syndrome with minor glomerular abnormality
N031Chronic nephritic syndrome with focal and segmental glomerular lesions
N032Chronic nephritic syndrome with diffuse membranous glomerulonephritis
N033Chronic nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
N034Chronic nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
N035Chronic nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
N036Chronic nephritic syndrome with dense deposit disease
N037Chronic nephritic syndrome with diffuse crescentic glomerulonephritis
N038Chronic nephritic syndrome with other morphologic changes
N039Chronic nephritic syndrome with unspecified morphologic changes
N03AChronic nephritic syndrome with C3 glomerulonephritis
N040Nephrotic syndrome with minor glomerular abnormality
N041Nephrotic syndrome with focal and segmental glomerular lesions
N0420Nephrotic syndrome with diffuse membranous glomerulonephritis, unspecified
N0421Primary membranous nephropathy with nephrotic syndrome
N0422Seconday membranous nephropathy with nephrotic syndrome
N0429Other nephrotic syndrome with diffuse membranous glomerulonephritis
N043Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis
N044Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritis
N045Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis
N046Nephrotic syndrome with dense deposit disease
N047Nephrotic syndrome with diffuse crescentic glomerulonephritis
N048Nephrotic syndrome with other morphologic changes
N049Nephrotic syndrome with unspecified morphologic changes
N04ANephrotic syndrome with C3 glomerulonephritis
N050Unspecified nephritic syndrome with minor glomerular abnormality
N051Unspecified nephritic syndrome with focal and segmental glomerular lesions
N052Unspecified nephritic syndrome with diffuse membranous glomerulonephritis
N053Unspecified nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
N054Unspecified nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
N055Unspecified nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
N056Unspecified nephritic syndrome with dense deposit disease
N057Unspecified nephritic syndrome with diffuse crescentic glomerulonephritis
N058Unspecified nephritic syndrome with other morphologic changes
N059Unspecified nephritic syndrome with unspecified morphologic changes
N05AUnspecified nephritic syndrome with C3 glomerulonephritis
N060Isolated proteinuria with minor glomerular abnormality
N061Isolated proteinuria with focal and segmental glomerular lesions
N0620Isolated proteinuria with diffuse membranous glomerulonephritis, unspecified
N0621Primary membranous nephropathy with isolated proteinuria
N0622Seconday membranous nephropathy with isolated proteinuria
N0629Other isolated proteinuria with diffuse membranous glomerulonephritis
N063Isolated proteinuria with diffuse mesangial proliferative glomerulonephritis
N064Isolated proteinuria with diffuse endocapillary proliferative glomerulonephritis
N065Isolated proteinuria with diffuse mesangiocapillary glomerulonephritis
N066Isolated proteinuria with dense deposit disease
N067Isolated proteinuria with diffuse crescentic glomerulonephritis
N068Isolated proteinuria with other morphologic lesion
N069Isolated proteinuria with unspecified morphologic lesion
N06AIsolated proteinuria with C3 glomerulonephritis
N070Hereditary nephropathy, not elsewhere classified with minor glomerular abnormality
N071Hereditary nephropathy, not elsewhere classified with focal and segmental glomerular lesions
N072Hereditary nephropathy, not elsewhere classified with diffuse membranous glomerulonephritis
N073Hereditary nephropathy, not elsewhere classified with diffuse mesangial proliferative glomerulonephritis
N074Hereditary nephropathy, not elsewhere classified with diffuse endocapillary proliferative glomerulonephritis
N075Hereditary nephropathy, not elsewhere classified with diffuse mesangiocapillary glomerulonephritis
N076Hereditary nephropathy, not elsewhere classified with dense deposit disease
N077Hereditary nephropathy, not elsewhere classified with diffuse crescentic glomerulonephritis
N078Hereditary nephropathy, not elsewhere classified with other morphologic lesions
N079Hereditary nephropathy, not elsewhere classified with unspecified morphologic lesions
N07AHereditary nephropathy, not elsewhere classified with C3 glomerulonephritis
N08Glomerular disorders in diseases classified elsewhere
N118Other chronic tubulo-interstitial nephritis
N119Chronic tubulo-interstitial nephritis, unspecified
N12Tubulo-interstitial nephritis, not specified as acute or chronic
N1411Contrast-induced nephropathy
N1419Nephropathy induced by other drugs, medicaments and biological substances
N170Acute kidney failure with tubular necrosis
N171Acute kidney failure with acute cortical necrosis
N172Acute kidney failure with medullary necrosis
N178Other acute kidney failure
N179Acute kidney failure, unspecified
N80A0Endometriosis of bladder, unspecified depth
N80A1Superficial endometriosis of bladder
N80A2Deep endometriosis of bladder
N80A41Superficial endometriosis of right ureter
N80A42Superficial endometriosis of left ureter
N80A43Superficial endometriosis of bilateral ureters
N80A49Superficial endometriosis of unspecified ureter
N80A51Deep endometriosis of right ureter
N80A52Deep endometriosis of left ureter
N80A53Deep endometriosis of bilateral ureters
N80A59Deep endometriosis of unspecified ureter
N80A61Endometriosis of right ureter, unspecified depth
N80A62Endometriosis of left ureter, unspecified depth
N80A63Endometriosis of bilateral ureters, unspecified depth
N80A69Endometriosis of unspecified ureter, unspecified depth
 
PDX Collection 6994
A150Tuberculosis of lung
A154Tuberculosis of intrathoracic lymph nodes
A155Tuberculosis of larynx, trachea and bronchus
A156Tuberculous pleurisy
A158Other respiratory tuberculosis
A159Respiratory tuberculosis unspecified
A179Tuberculosis of nervous system, unspecified
A1882Tuberculosis of other endocrine glands
A1884Tuberculosis of heart
A1889Tuberculosis of other sites
A212Pulmonary tularemia
A221Pulmonary anthrax
A310Pulmonary mycobacterial infection
A3701Whooping cough due to Bordetella pertussis with pneumonia
A3711Whooping cough due to Bordetella parapertussis with pneumonia
A3781Whooping cough due to other Bordetella species with pneumonia
A3791Whooping cough, unspecified species with pneumonia
A420Pulmonary actinomycosis
A430Pulmonary nocardiosis
A481Legionnaires' disease
B250Cytomegaloviral pneumonitis
B390Acute pulmonary histoplasmosis capsulati
B391Chronic pulmonary histoplasmosis capsulati
B392Pulmonary histoplasmosis capsulati, unspecified
B440Invasive pulmonary aspergillosis
B583Pulmonary toxoplasmosis
B59Pneumocystosis
B671Echinococcus granulosus infection of lung
J09X1Influenza due to identified novel influenza A virus with pneumonia
J09X2Influenza due to identified novel influenza A virus with other respiratory manifestations
J1000Influenza due to other identified influenza virus with unspecified type of pneumonia
J1001Influenza due to other identified influenza virus with the same other identified influenza virus pneumonia
J1008Influenza due to other identified influenza virus with other specified pneumonia
J101Influenza due to other identified influenza virus with other respiratory manifestations
J1100Influenza due to unidentified influenza virus with unspecified type of pneumonia
J1108Influenza due to unidentified influenza virus with specified pneumonia
J111Influenza due to unidentified influenza virus with other respiratory manifestations
J120Adenoviral pneumonia
J121Respiratory syncytial virus pneumonia
J122Parainfluenza virus pneumonia
J123Human metapneumovirus pneumonia
J1289Other viral pneumonia
J129Viral pneumonia, unspecified
J13Pneumonia due to Streptococcus pneumoniae
J14Pneumonia due to Hemophilus influenzae
J150Pneumonia due to Klebsiella pneumoniae
J151Pneumonia due to Pseudomonas
J1520Pneumonia due to staphylococcus, unspecified
J15211Pneumonia due to Methicillin susceptible Staphylococcus aureus
J15212Pneumonia due to Methicillin resistant Staphylococcus aureus
J1529Pneumonia due to other staphylococcus
J153Pneumonia due to streptococcus, group B
J154Pneumonia due to other streptococci
J155Pneumonia due to Escherichia coli
J1561Pneumonia due to Acinetobacter baumannii
J1569Pneumonia due to other Gram-negative bacteria
J157Pneumonia due to Mycoplasma pneumoniae
J158Pneumonia due to other specified bacteria
J159Unspecified bacterial pneumonia
J160Chlamydial pneumonia
J168Pneumonia due to other specified infectious organisms
J17Pneumonia in diseases classified elsewhere
J180Bronchopneumonia, unspecified organism
J181Lobar pneumonia, unspecified organism
J188Other pneumonia, unspecified organism



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