ICD-10-CM/PCS MS-DRG v42.0 Definitions Manual

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Appendix C: Principal diagnoses which convert CC/MCC to non-CC
Page 65 of 431
PDX Collection 0627 (continued)
E7602Hurler-Scheie syndrome
E7603Scheie's syndrome
E761Mucopolysaccharidosis, type II
E76210Morquio A mucopolysaccharidoses
E76211Morquio B mucopolysaccharidoses
E76219Morquio mucopolysaccharidoses, unspecified
E7622Sanfilippo mucopolysaccharidoses
E7629Other mucopolysaccharidoses
E763Mucopolysaccharidosis, unspecified
E768Other disorders of glucosaminoglycan metabolism
E769Glucosaminoglycan metabolism disorder, unspecified
E791Lesch-Nyhan syndrome
E792Myoadenylate deaminase deficiency
E7981Aicardi-Goutieres syndrome
E7982Hereditary xanthinuria
E7989Other specified disorders of purine and pyrimidine metabolism
E799Disorder of purine and pyrimidine metabolism, unspecified
E800Hereditary erythropoietic porphyria
E801Porphyria cutanea tarda
E8020Unspecified porphyria
E8021Acute intermittent (hepatic) porphyria
E8029Other porphyria
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E850Non-neuropathic heredofamilial amyloidosis
E859Amyloidosis, unspecified
E88810Metabolic syndrome
 
PDX Collection 0628
E7871Barth syndrome
E7872Smith-Lemli-Opitz syndrome
Q8711Prader-Willi syndrome
Q8719Other congenital malformation syndromes predominantly associated with short stature
Q872Congenital malformation syndromes predominantly involving limbs
Q873Congenital malformation syndromes involving early overgrowth
Q8740Marfan syndrome, unspecified
Q87410Marfan syndrome with aortic dilation
Q87418Marfan syndrome with other cardiovascular manifestations
Q8742Marfan syndrome with ocular manifestations
Q8743Marfan syndrome with skeletal manifestation
Q875Other congenital malformation syndromes with other skeletal changes
Q8781Alport syndrome
Q8782Arterial tortuosity syndrome
Q8783Bardet-Biedl syndrome
Q8784Laurence-Moon syndrome
Q8785MED13L syndrome
Q8786Kleefstra syndrome
Q8789Other specified congenital malformation syndromes, not elsewhere classified
Q898Other specified congenital malformations
Q992Fragile X chromosome
 
PDX Collection 0629
E71310Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311Medium chain acyl CoA dehydrogenase deficiency
E71312Short chain acyl CoA dehydrogenase deficiency
E71313Glutaric aciduria type II
E71314Muscle carnitine palmitoyltransferase deficiency
E71318Other disorders of fatty-acid oxidation
E7132Disorders of ketone metabolism
E7140Disorder of carnitine metabolism, unspecified
E7141Primary carnitine deficiency
E7142Carnitine deficiency due to inborn errors of metabolism
E7143Iatrogenic carnitine deficiency
E71440Ruvalcaba-Myhre-Smith syndrome
E71448Other secondary carnitine deficiency
E7150Peroxisomal disorder, unspecified
E71510Zellweger syndrome
E71511Neonatal adrenoleukodystrophy
E71518Other disorders of peroxisome biogenesis
E71520Childhood cerebral X-linked adrenoleukodystrophy
E71521Adolescent X-linked adrenoleukodystrophy
E71522Adrenomyeloneuropathy
E71528Other X-linked adrenoleukodystrophy
E71529X-linked adrenoleukodystrophy, unspecified type
E7153Other group 2 peroxisomal disorders
E71540Rhizomelic chondrodysplasia punctata
E71541Zellweger-like syndrome
E71542Other group 3 peroxisomal disorders
E71548Other peroxisomal disorders
E803Defects of catalase and peroxidase
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E8840Mitochondrial metabolism disorder, unspecified
E8841MELAS syndrome
E8842MERRF syndrome
E8843Disorders of mitochondrial tRNA synthetases
E8849Other mitochondrial metabolism disorders
H49811Kearns-Sayre syndrome, right eye
H49812Kearns-Sayre syndrome, left eye
H49813Kearns-Sayre syndrome, bilateral
H49819Kearns-Sayre syndrome, unspecified eye
 
PDX Collection 0630
E840Cystic fibrosis with pulmonary manifestations
E8411Meconium ileus in cystic fibrosis
E8419Cystic fibrosis with other intestinal manifestations
E848Cystic fibrosis with other manifestations
E849Cystic fibrosis, unspecified
 
PDX Collection 0631
E850Non-neuropathic heredofamilial amyloidosis
E851Neuropathic heredofamilial amyloidosis
E852Heredofamilial amyloidosis, unspecified
E853Secondary systemic amyloidosis
E854Organ-limited amyloidosis
E8581Light chain (AL) amyloidosis
E8582Wild-type transthyretin-related (ATTR) amyloidosis
E8589Other amyloidosis
E859Amyloidosis, unspecified
E88810Metabolic syndrome
 
PDX Collection 0632
E860Dehydration
E861Hypovolemia
E869Volume depletion, unspecified
E870Hyperosmolality and hypernatremia
E871Hypo-osmolality and hyponatremia
E8720Acidosis, unspecified
E8721Acute metabolic acidosis
E8722Chronic metabolic acidosis
E8729Other acidosis
E873Alkalosis
E874Mixed disorder of acid-base balance
E875Hyperkalemia
E876Hypokalemia
E8770Fluid overload, unspecified
E8771Transfusion associated circulatory overload
E8779Other fluid overload
E878Other disorders of electrolyte and fluid balance, not elsewhere classified
 
PDX Collection 0633
C8800Waldenstrom macroglobulinemia not having achieved remission
C8801Waldenstrom macroglobulinemia, in remission
D472Monoclonal gammopathy
D890Polyclonal hypergammaglobulinemia
D891Cryoglobulinemia
E700Classical phenylketonuria
E701Other hyperphenylalaninemias
E7020Disorder of tyrosine metabolism, unspecified
E7021Tyrosinemia
E7029Other disorders of tyrosine metabolism
E7030Albinism, unspecified
E70310X-linked ocular albinism
E70311Autosomal recessive ocular albinism
E70318Other ocular albinism
E70319Ocular albinism, unspecified
E70320Tyrosinase negative oculocutaneous albinism
E70321Tyrosinase positive oculocutaneous albinism
E70328Other oculocutaneous albinism
E70329Oculocutaneous albinism, unspecified
E70330Chediak-Higashi syndrome
E70331Hermansky-Pudlak syndrome
E70338Other albinism with hematologic abnormality
E70339Albinism with hematologic abnormality, unspecified
E7039Other specified albinism
E7040Disorders of histidine metabolism, unspecified
E7041Histidinemia
E7049Other disorders of histidine metabolism
E705Disorders of tryptophan metabolism
E7081Aromatic L-amino acid decarboxylase deficiency
E7089Other disorders of aromatic amino-acid metabolism
E709Disorder of aromatic amino-acid metabolism, unspecified
E710Maple-syrup-urine disease
E71110Isovaleric acidemia
E711113-methylglutaconic aciduria
E71118Other branched-chain organic acidurias
E71120Methylmalonic acidemia
E71121Propionic acidemia
E71128Other disorders of propionate metabolism
E7119Other disorders of branched-chain amino-acid metabolism
E712Disorder of branched-chain amino-acid metabolism, unspecified
E7130Disorder of fatty-acid metabolism, unspecified
E7200Disorders of amino-acid transport, unspecified
E7201Cystinuria
E7202Hartnup's disease
E7204Cystinosis
E7209Other disorders of amino-acid transport
E7210Disorders of sulfur-bearing amino-acid metabolism, unspecified
E7211Homocystinuria
E7212Methylenetetrahydrofolate reductase deficiency
E7219Other disorders of sulfur-bearing amino-acid metabolism
E7220Disorder of urea cycle metabolism, unspecified
E7221Argininemia
E7222Arginosuccinic aciduria
E7223Citrullinemia
E7229Other disorders of urea cycle metabolism
E723Disorders of lysine and hydroxylysine metabolism
E724Disorders of ornithine metabolism
E7250Disorder of glycine metabolism, unspecified
E7251Non-ketotic hyperglycinemia
E7252Trimethylaminuria
E7253Primary hyperoxaluria
E7259Other disorders of glycine metabolism
E7281Disorders of gamma aminobutyric acid metabolism
E7289Other specified disorders of amino-acid metabolism
E729Disorder of amino-acid metabolism, unspecified
E730Congenital lactase deficiency
E731Secondary lactase deficiency
E738Other lactose intolerance
E739Lactose intolerance, unspecified
E7400Glycogen storage disease, unspecified
E7401von Gierke disease
E7402Pompe disease
E7403Cori disease
E7404McArdle disease
E7405Lysosome-associated membrane protein 2 [LAMP2] deficiency
E7409Other glycogen storage disease
E7410Disorder of fructose metabolism, unspecified
E7411Essential fructosuria
E7412Hereditary fructose intolerance
E7419Other disorders of fructose metabolism
E7420Disorders of galactose metabolism, unspecified
E7421Galactosemia
E7429Other disorders of galactose metabolism
E7431Sucrase-isomaltase deficiency
E7439Other disorders of intestinal carbohydrate absorption
E744Disorders of pyruvate metabolism and gluconeogenesis
E74810Glucose transporter protein type 1 deficiency
E74818Other disorders of glucose transport
E74819Disorders of glucose transport, unspecified
E74820SLC13A5 Citrate Transporter Disorder
E74829Other disorders of citrate metabolism
E7489Other specified disorders of carbohydrate metabolism
E749Disorder of carbohydrate metabolism, unspecified
E7521Fabry (-Anderson) disease
E7522Gaucher disease
E75240Niemann-Pick disease type A
E75241Niemann-Pick disease type B
E75242Niemann-Pick disease type C
E75243Niemann-Pick disease type D
E75244Niemann-Pick disease type A/B
E75248Other Niemann-Pick disease
E75249Niemann-Pick disease, unspecified
E753Sphingolipidosis, unspecified
E755Other lipid storage disorders
E756Lipid storage disorder, unspecified
E770Defects in post-translational modification of lysosomal enzymes
E771Defects in glycoprotein degradation
E778Other disorders of glycoprotein metabolism
E779Disorder of glycoprotein metabolism, unspecified
E7800Pure hypercholesterolemia, unspecified
E7801Familial hypercholesterolemia
E781Pure hyperglyceridemia
E782Mixed hyperlipidemia
E783Hyperchylomicronemia
E7841Elevated Lipoprotein(a)
E7849Other hyperlipidemia
E785Hyperlipidemia, unspecified
E786Lipoprotein deficiency
E7870Disorder of bile acid and cholesterol metabolism, unspecified
E7879Other disorders of bile acid and cholesterol metabolism
E7881Lipoid dermatoarthritis
E7889Other lipoprotein metabolism disorders
E789Disorder of lipoprotein metabolism, unspecified
E8802Plasminogen deficiency
E8809Other disorders of plasma-protein metabolism, not elsewhere classified
E881Lipodystrophy, not elsewhere classified
E882Lipomatosis, not elsewhere classified
 
PDX Collection 0634
E0921Drug or chemical induced diabetes mellitus with diabetic nephropathy
E0922Drug or chemical induced diabetes mellitus with diabetic chronic kidney disease
E0929Drug or chemical induced diabetes mellitus with other diabetic kidney complication
E883Tumor lysis syndrome
N000Acute nephritic syndrome with minor glomerular abnormality
N001Acute nephritic syndrome with focal and segmental glomerular lesions
N002Acute nephritic syndrome with diffuse membranous glomerulonephritis
N003Acute nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
N004Acute nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
N005Acute nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
N006Acute nephritic syndrome with dense deposit disease
N007Acute nephritic syndrome with diffuse crescentic glomerulonephritis
N008Acute nephritic syndrome with other morphologic changes
N009Acute nephritic syndrome with unspecified morphologic changes
N00AAcute nephritic syndrome with C3 glomerulonephritis
N010Rapidly progressive nephritic syndrome with minor glomerular abnormality
N011Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions
N012Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis
N013Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
N014Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
N015Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
N016Rapidly progressive nephritic syndrome with dense deposit disease
N017Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis
N018Rapidly progressive nephritic syndrome with other morphologic changes
N019Rapidly progressive nephritic syndrome with unspecified morphologic changes
N01ARapidly progressive nephritic syndrome with C3 glomerulonephritis
N028Recurrent and persistent hematuria with other morphologic changes
N029Recurrent and persistent hematuria with unspecified morphologic changes
N02ARecurrent and persistent hematuria with C3 glomerulonephritis
N02B1Recurrent and persistent immunoglobulin A nephropathy with glomerular lesion
N02B2Recurrent and persistent immunoglobulin A nephropathy with focal and segmental glomerular lesion
N02B3Recurrent and persistent immunoglobulin A nephropathy with diffuse membranoproliferative glomerulonephritis
N02B4Recurrent and persistent immunoglobulin A nephropathy with diffuse membranous glomerulonephritis
N02B5Recurrent and persistent immunoglobulin A nephropathy with diffuse mesangial proliferative glomerulonephritis
N02B6Recurrent and persistent immunoglobulin A nephropathy with diffuse mesangiocapillary glomerulonephritis
N02B9Other recurrent and persistent immunoglobulin A nephropathy
N047Nephrotic syndrome with diffuse crescentic glomerulonephritis
N048Nephrotic syndrome with other morphologic changes
N049Nephrotic syndrome with unspecified morphologic changes
N04ANephrotic syndrome with C3 glomerulonephritis
N050Unspecified nephritic syndrome with minor glomerular abnormality
N051Unspecified nephritic syndrome with focal and segmental glomerular lesions
N056Unspecified nephritic syndrome with dense deposit disease
N057Unspecified nephritic syndrome with diffuse crescentic glomerulonephritis
N058Unspecified nephritic syndrome with other morphologic changes
N059Unspecified nephritic syndrome with unspecified morphologic changes
N05AUnspecified nephritic syndrome with C3 glomerulonephritis
N060Isolated proteinuria with minor glomerular abnormality
N061Isolated proteinuria with focal and segmental glomerular lesions
N066Isolated proteinuria with dense deposit disease
N067Isolated proteinuria with diffuse crescentic glomerulonephritis
N068Isolated proteinuria with other morphologic lesion
N069Isolated proteinuria with unspecified morphologic lesion
N070Hereditary nephropathy, not elsewhere classified with minor glomerular abnormality
N071Hereditary nephropathy, not elsewhere classified with focal and segmental glomerular lesions
N076Hereditary nephropathy, not elsewhere classified with dense deposit disease
N077Hereditary nephropathy, not elsewhere classified with diffuse crescentic glomerulonephritis
N078Hereditary nephropathy, not elsewhere classified with other morphologic lesions
N079Hereditary nephropathy, not elsewhere classified with unspecified morphologic lesions
N140Analgesic nephropathy
N1411Contrast-induced nephropathy
N1419Nephropathy induced by other drugs, medicaments and biological substances
N142Nephropathy induced by unspecified drug, medicament or biological substance
N143Nephropathy induced by heavy metals
N144Toxic nephropathy, not elsewhere classified
N150Balkan nephropathy
N158Other specified renal tubulo-interstitial diseases
N159Renal tubulo-interstitial disease, unspecified
N170Acute kidney failure with tubular necrosis
N171Acute kidney failure with acute cortical necrosis
N172Acute kidney failure with medullary necrosis
N178Other acute kidney failure
N179Acute kidney failure, unspecified
 
PDX Collection 0635
C965Multifocal and unisystemic Langerhans-cell histiocytosis
C966Unifocal Langerhans-cell histiocytosis
E71310Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311Medium chain acyl CoA dehydrogenase deficiency
E71312Short chain acyl CoA dehydrogenase deficiency
E71313Glutaric aciduria type II
E71314Muscle carnitine palmitoyltransferase deficiency
E71318Other disorders of fatty-acid oxidation
E7132Disorders of ketone metabolism
E7139Other disorders of fatty-acid metabolism
E7140Disorder of carnitine metabolism, unspecified
E7141Primary carnitine deficiency
E7142Carnitine deficiency due to inborn errors of metabolism
E7143Iatrogenic carnitine deficiency
E71440Ruvalcaba-Myhre-Smith syndrome
E71448Other secondary carnitine deficiency
E7150Peroxisomal disorder, unspecified
E71510Zellweger syndrome
E71511Neonatal adrenoleukodystrophy
E71518Other disorders of peroxisome biogenesis
E71520Childhood cerebral X-linked adrenoleukodystrophy
E71521Adolescent X-linked adrenoleukodystrophy
E71522Adrenomyeloneuropathy
E71528Other X-linked adrenoleukodystrophy
E71529X-linked adrenoleukodystrophy, unspecified type
E7153Other group 2 peroxisomal disorders
E71540Rhizomelic chondrodysplasia punctata
E71541Zellweger-like syndrome
E71542Other group 3 peroxisomal disorders
E71548Other peroxisomal disorders
E803Defects of catalase and peroxidase
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E8840Mitochondrial metabolism disorder, unspecified
E88811Insulin resistance syndrome, Type A
E88818Other insulin resistance
E88819Insulin resistance, unspecified
E8882Obesity due to disruption of MC4R pathway
E8889Other specified metabolic disorders
 
PDX Collection 0636
C965Multifocal and unisystemic Langerhans-cell histiocytosis
C966Unifocal Langerhans-cell histiocytosis
E71310Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311Medium chain acyl CoA dehydrogenase deficiency
E71312Short chain acyl CoA dehydrogenase deficiency
E71313Glutaric aciduria type II
E71314Muscle carnitine palmitoyltransferase deficiency
E71318Other disorders of fatty-acid oxidation
E7132Disorders of ketone metabolism
E7139Other disorders of fatty-acid metabolism
E7140Disorder of carnitine metabolism, unspecified
E7141Primary carnitine deficiency
E7142Carnitine deficiency due to inborn errors of metabolism
E7143Iatrogenic carnitine deficiency
E71440Ruvalcaba-Myhre-Smith syndrome
E71448Other secondary carnitine deficiency
E7150Peroxisomal disorder, unspecified
E71510Zellweger syndrome
E71511Neonatal adrenoleukodystrophy
E71518Other disorders of peroxisome biogenesis
E71520Childhood cerebral X-linked adrenoleukodystrophy
E71521Adolescent X-linked adrenoleukodystrophy
E71522Adrenomyeloneuropathy
E71528Other X-linked adrenoleukodystrophy
E71529X-linked adrenoleukodystrophy, unspecified type
E7153Other group 2 peroxisomal disorders
E71540Rhizomelic chondrodysplasia punctata
E71541Zellweger-like syndrome
E71542Other group 3 peroxisomal disorders
E71548Other peroxisomal disorders
E803Defects of catalase and peroxidase
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E8841MELAS syndrome



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