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ICD-10-CM/PCS MS-DRGv33 Definitions Manual Previous Page [Alt-p] Up a level [Alt-u] Next Page [Alt-n]
Appendix C: Principal diagnoses which convert CC/MCC to non-CC
PDX Collection 0538:28 codes
E7500GM2 gangliosidosis, unspecified
E7501Sandhoff disease
E7502Tay-Sachs disease
E7509Other GM2 gangliosidosis
E7510Unspecified gangliosidosis
E7511Mucolipidosis IV
E7519Other gangliosidosis
E7523Krabbe disease
E7525Metachromatic leukodystrophy
E7529Other sphingolipidosis
E754Neuronal ceroid lipofuscinosis
F842Rett's syndrome
G132Systemic atrophy primarily affecting the central nervous system in myxedema
G138Systemic atrophy primarily affecting central nervous system in other diseases classified elsewhere
G312Degeneration of nervous system due to alcohol
G3181Alpers disease
G3182Leigh's disease
G3289Other specified degenerative disorders of nervous system in diseases classified elsewhere
G914Hydrocephalus in diseases classified elsewhere
G9381Temporal sclerosis
G9389Other specified disorders of brain
G939Disorder of brain, unspecified
G94Other disorders of brain in diseases classified elsewhere
G968Other specified disorders of central nervous system
G969Disorder of central nervous system, unspecified
G980Neurogenic arthritis, not elsewhere classified
G988Other disorders of nervous system
G998Other specified disorders of nervous system in diseases classified elsewhere
 
PDX Collection 0539:32 codes
D813Adenosine deaminase [ADA] deficiency
D815Purine nucleoside phosphorylase [PNP] deficiency
D81810Biotinidase deficiency
D841Defects in the complement system
E7601Hurler's syndrome
E7602Hurler-Scheie syndrome
E7603Scheie's syndrome
E761Mucopolysaccharidosis, type II
E76210Morquio A mucopolysaccharidoses
E76211Morquio B mucopolysaccharidoses
E76219Morquio mucopolysaccharidoses, unspecified
E7622Sanfilippo mucopolysaccharidoses
E7629Other mucopolysaccharidoses
E763Mucopolysaccharidosis, unspecified
E768Other disorders of glucosaminoglycan metabolism
E769Glucosaminoglycan metabolism disorder, unspecified
E791Lesch-Nyhan syndrome
E792Myoadenylate deaminase deficiency
E798Other disorders of purine and pyrimidine metabolism
E799Disorder of purine and pyrimidine metabolism, unspecified
E800Hereditary erythropoietic porphyria
E801Porphyria cutanea tarda
E8020Unspecified porphyria
E8021Acute intermittent (hepatic) porphyria
E8029Other porphyria
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E850Non-neuropathic heredofamilial amyloidosis
E859Amyloidosis, unspecified
E8881Metabolic syndrome
 
PDX Collection 0540:15 codes
E7871Barth syndrome
E7872Smith-Lemli-Opitz syndrome
Q871Congenital malformation syndromes predominantly associated with short stature
Q872Congenital malformation syndromes predominantly involving limbs
Q873Congenital malformation syndromes involving early overgrowth
Q8740Marfan's syndrome, unspecified
Q87410Marfan's syndrome with aortic dilation
Q87418Marfan's syndrome with other cardiovascular manifestations
Q8742Marfan's syndrome with ocular manifestations
Q8743Marfan's syndrome with skeletal manifestation
Q875Other congenital malformation syndromes with other skeletal changes
Q8781Alport syndrome
Q8789Other specified congenital malformation syndromes, not elsewhere classified
Q898Other specified congenital malformations
Q992Fragile X chromosome
 
PDX Collection 0541:5 codes
E840Cystic fibrosis with pulmonary manifestations
E8411Meconium ileus in cystic fibrosis
E8419Cystic fibrosis with other intestinal manifestations
E848Cystic fibrosis with other manifestations
E849Cystic fibrosis, unspecified
 
PDX Collection 0542:8 codes
E850Non-neuropathic heredofamilial amyloidosis
E851Neuropathic heredofamilial amyloidosis
E852Heredofamilial amyloidosis, unspecified
E853Secondary systemic amyloidosis
E854Organ-limited amyloidosis
E858Other amyloidosis
E859Amyloidosis, unspecified
E8881Metabolic syndrome
 
PDX Collection 0543:14 codes
E860Dehydration
E861Hypovolemia
E869Volume depletion, unspecified
E870Hyperosmolality and hypernatremia
E871Hypo-osmolality and hyponatremia
E872Acidosis
E873Alkalosis
E874Mixed disorder of acid-base balance
E875Hyperkalemia
E876Hypokalemia
E8770Fluid overload, unspecified
E8771Transfusion associated circulatory overload
E8779Other fluid overload
E878Other disorders of electrolyte and fluid balance, not elsewhere classified
 
PDX Collection 0544:65 codes
E0821Diabetes mellitus due to underlying condition with diabetic nephropathy
E0822Diabetes mellitus due to underlying condition with diabetic chronic kidney disease
E0829Diabetes mellitus due to underlying condition with other diabetic kidney complication
E0921Drug or chemical induced diabetes mellitus with diabetic nephropathy
E0922Drug or chemical induced diabetes mellitus with diabetic chronic kidney disease
E0929Drug or chemical induced diabetes mellitus with other diabetic kidney complication
E883Tumor lysis syndrome
N000Acute nephritic syndrome with minor glomerular abnormality
N001Acute nephritic syndrome with focal and segmental glomerular lesions
N002Acute nephritic syndrome with diffuse membranous glomerulonephritis
N003Acute nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
N004Acute nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
N005Acute nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
N006Acute nephritic syndrome with dense deposit disease
N007Acute nephritic syndrome with diffuse crescentic glomerulonephritis
N008Acute nephritic syndrome with other morphologic changes
N009Acute nephritic syndrome with unspecified morphologic changes
N010Rapidly progressive nephritic syndrome with minor glomerular abnormality
N011Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions
N012Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis
N013Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
N014Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
N015Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
N016Rapidly progressive nephritic syndrome with dense deposit disease
N017Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis
N018Rapidly progressive nephritic syndrome with other morphologic changes
N019Rapidly progressive nephritic syndrome with unspecified morphologic changes
N028Recurrent and persistent hematuria with other morphologic changes
N029Recurrent and persistent hematuria with unspecified morphologic changes
N047Nephrotic syndrome with diffuse crescentic glomerulonephritis
N048Nephrotic syndrome with other morphologic changes
N049Nephrotic syndrome with unspecified morphologic changes
N050Unspecified nephritic syndrome with minor glomerular abnormality
N051Unspecified nephritic syndrome with focal and segmental glomerular lesions
N056Unspecified nephritic syndrome with dense deposit disease
N057Unspecified nephritic syndrome with diffuse crescentic glomerulonephritis
N058Unspecified nephritic syndrome with other morphologic changes
N059Unspecified nephritic syndrome with unspecified morphologic changes
N060Isolated proteinuria with minor glomerular abnormality
N061Isolated proteinuria with focal and segmental glomerular lesions
N066Isolated proteinuria with dense deposit disease
N067Isolated proteinuria with diffuse crescentic glomerulonephritis
N068Isolated proteinuria with other morphologic lesion
N069Isolated proteinuria with unspecified morphologic lesion
N070Hereditary nephropathy, not elsewhere classified with minor glomerular abnormality
N071Hereditary nephropathy, not elsewhere classified with focal and segmental glomerular lesions
N076Hereditary nephropathy, not elsewhere classified with dense deposit disease
N077Hereditary nephropathy, not elsewhere classified with diffuse crescentic glomerulonephritis
N078Hereditary nephropathy, not elsewhere classified with other morphologic lesions
N079Hereditary nephropathy, not elsewhere classified with unspecified morphologic lesions
N08Glomerular disorders in diseases classified elsewhere
N140Analgesic nephropathy
N141Nephropathy induced by other drugs, medicaments and biological substances
N142Nephropathy induced by unspecified drug, medicament or biological substance
N143Nephropathy induced by heavy metals
N144Toxic nephropathy, not elsewhere classified
N150Balkan nephropathy
N158Other specified renal tubulo-interstitial diseases
N159Renal tubulo-interstitial disease, unspecified
N16Renal tubulo-interstitial disorders in diseases classified elsewhere
N170Acute kidney failure with tubular necrosis
N171Acute kidney failure with acute cortical necrosis
N172Acute kidney failure with medullary necrosis
N178Other acute kidney failure
N179Acute kidney failure, unspecified
 
PDX Collection 0545:36 codes
C965Multifocal and unisystemic Langerhans-cell histiocytosis
C966Unifocal Langerhans-cell histiocytosis
E71310Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311Medium chain acyl CoA dehydrogenase deficiency
E71312Short chain acyl CoA dehydrogenase deficiency
E71313Glutaric aciduria type II
E71314Muscle carnitine palmitoyltransferase deficiency
E71318Other disorders of fatty-acid oxidation
E7132Disorders of ketone metabolism
E7139Other disorders of fatty-acid metabolism
E7140Disorder of carnitine metabolism, unspecified
E7141Primary carnitine deficiency
E7142Carnitine deficiency due to inborn errors of metabolism
E7143Iatrogenic carnitine deficiency
E71440Ruvalcaba-Myhre-Smith syndrome
E71448Other secondary carnitine deficiency
E7150Peroxisomal disorder, unspecified
E71510Zellweger syndrome
E71511Neonatal adrenoleukodystrophy
E71518Other disorders of peroxisome biogenesis
E71520Childhood cerebral X-linked adrenoleukodystrophy
E71521Adolescent X-linked adrenoleukodystrophy
E71522Adrenomyeloneuropathy
E71528Other X-linked adrenoleukodystrophy
E71529X-linked adrenoleukodystrophy, unspecified type
E7153Other group 2 peroxisomal disorders
E71540Rhizomelic chondrodysplasia punctata
E71541Zellweger-like syndrome
E71542Other group 3 peroxisomal disorders
E71548Other peroxisomal disorders
E803Defects of catalase and peroxidase
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E8889Other specified metabolic disorders
 
PDX Collection 0546:20 codes
E368Other intraoperative complications of endocrine system
E89810Postprocedural hemorrhage and hematoma of an endocrine system organ or structure following an endocrine system procedure
E89811Postprocedural hemorrhage and hematoma of an endocrine system organ or structure following other procedure
E8989Other postprocedural endocrine and metabolic complications and disorders
H95811Postprocedural stenosis of right external ear canal
H95812Postprocedural stenosis of left external ear canal
H95813Postprocedural stenosis of external ear canal, bilateral
H95819Postprocedural stenosis of unspecified external ear canal
H9588Other intraoperative complications and disorders of the ear and mastoid process, not elsewhere classified
H9589Other postprocedural complications and disorders of the ear and mastoid process, not elsewhere classified
I973Postprocedural hypertension
M9689Other intraoperative and postprocedural complications and disorders of the musculoskeletal system
N981Hyperstimulation of ovaries
N982Complications of attempted introduction of fertilized ovum following in vitro fertilization
N983Complications of attempted introduction of embryo in embryo transfer
N988Other complications associated with artificial fertilization
N989Complication associated with artificial fertilization, unspecified
T8182XAEmphysema (subcutaneous) resulting from a procedure, initial encounter
T8189XAOther complications of procedures, not elsewhere classified, initial encounter
T819XXAUnspecified complication of procedure, initial encounter
 
PDX Collection 0547:1 code
F0151Vascular dementia with behavioral disturbance
 
PDX Collection 0548:2 codes
F0281Dementia in other diseases classified elsewhere with behavioral disturbance
F0391Unspecified dementia with behavioral disturbance
 
PDX Collection 0549:2 codes
F05Delirium due to known physiological condition
R45851Suicidal ideations



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