ICD-10-CM/PCS MS-DRG v38.1 Definitions Manual

Appendix C: Principal diagnoses which convert CC/MCC to non-CC

Page 351 of 454

PDX Collection 3648 (continued)
E7153	Other group 2 peroxisomal disorders
E71540	Rhizomelic chondrodysplasia punctata
E71541	Zellweger-like syndrome
E71542	Other group 3 peroxisomal disorders
E71548	Other peroxisomal disorders
E804	Gilbert syndrome
E805	Crigler-Najjar syndrome
E806	Other disorders of bilirubin metabolism
E807	Disorder of bilirubin metabolism, unspecified
E8840	Mitochondrial metabolism disorder, unspecified
E8841	MELAS syndrome
E8842	MERRF syndrome
E8849	Other mitochondrial metabolism disorders
H49811	Kearns-Sayre syndrome, right eye
H49812	Kearns-Sayre syndrome, left eye
H49813	Kearns-Sayre syndrome, bilateral
H49819	Kearns-Sayre syndrome, unspecified eye

PDX Collection 3650
C965	Multifocal and unisystemic Langerhans-cell histiocytosis
C966	Unifocal Langerhans-cell histiocytosis
E71310	Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311	Medium chain acyl CoA dehydrogenase deficiency
E71312	Short chain acyl CoA dehydrogenase deficiency
E71313	Glutaric aciduria type II
E71314	Muscle carnitine palmitoyltransferase deficiency
E71318	Other disorders of fatty-acid oxidation
E7132	Disorders of ketone metabolism
E7139	Other disorders of fatty-acid metabolism
E7140	Disorder of carnitine metabolism, unspecified
E7141	Primary carnitine deficiency
E7142	Carnitine deficiency due to inborn errors of metabolism
E7143	Iatrogenic carnitine deficiency
E71440	Ruvalcaba-Myhre-Smith syndrome
E71448	Other secondary carnitine deficiency
E7150	Peroxisomal disorder, unspecified
E803	Defects of catalase and peroxidase
E804	Gilbert syndrome
E805	Crigler-Najjar syndrome
E806	Other disorders of bilirubin metabolism
E807	Disorder of bilirubin metabolism, unspecified
E8840	Mitochondrial metabolism disorder, unspecified
E8841	MELAS syndrome
E8842	MERRF syndrome
E8849	Other mitochondrial metabolism disorders
E8889	Other specified metabolic disorders
H49811	Kearns-Sayre syndrome, right eye
H49812	Kearns-Sayre syndrome, left eye
H49813	Kearns-Sayre syndrome, bilateral
H49819	Kearns-Sayre syndrome, unspecified eye

PDX Collection 3652
C965	Multifocal and unisystemic Langerhans-cell histiocytosis
C966	Unifocal Langerhans-cell histiocytosis
E71310	Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311	Medium chain acyl CoA dehydrogenase deficiency
E71312	Short chain acyl CoA dehydrogenase deficiency
E71313	Glutaric aciduria type II
E71314	Muscle carnitine palmitoyltransferase deficiency
E71318	Other disorders of fatty-acid oxidation
E7132	Disorders of ketone metabolism
E7139	Other disorders of fatty-acid metabolism
E7140	Disorder of carnitine metabolism, unspecified
E7141	Primary carnitine deficiency
E7142	Carnitine deficiency due to inborn errors of metabolism
E7143	Iatrogenic carnitine deficiency
E71440	Ruvalcaba-Myhre-Smith syndrome
E71448	Other secondary carnitine deficiency
E71510	Zellweger syndrome
E803	Defects of catalase and peroxidase
E804	Gilbert syndrome
E805	Crigler-Najjar syndrome
E806	Other disorders of bilirubin metabolism
E807	Disorder of bilirubin metabolism, unspecified
E8840	Mitochondrial metabolism disorder, unspecified
E8841	MELAS syndrome
E8842	MERRF syndrome
E8849	Other mitochondrial metabolism disorders
E8889	Other specified metabolic disorders
H49811	Kearns-Sayre syndrome, right eye
H49812	Kearns-Sayre syndrome, left eye
H49813	Kearns-Sayre syndrome, bilateral
H49819	Kearns-Sayre syndrome, unspecified eye

PDX Collection 3654
C965	Multifocal and unisystemic Langerhans-cell histiocytosis
C966	Unifocal Langerhans-cell histiocytosis
E71310	Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311	Medium chain acyl CoA dehydrogenase deficiency
E71312	Short chain acyl CoA dehydrogenase deficiency
E71313	Glutaric aciduria type II
E71314	Muscle carnitine palmitoyltransferase deficiency
E71318	Other disorders of fatty-acid oxidation
E7132	Disorders of ketone metabolism
E7139	Other disorders of fatty-acid metabolism
E7140	Disorder of carnitine metabolism, unspecified
E7141	Primary carnitine deficiency
E7142	Carnitine deficiency due to inborn errors of metabolism
E7143	Iatrogenic carnitine deficiency
E71440	Ruvalcaba-Myhre-Smith syndrome
E71448	Other secondary carnitine deficiency
E71511	Neonatal adrenoleukodystrophy
E803	Defects of catalase and peroxidase
E804	Gilbert syndrome
E805	Crigler-Najjar syndrome
E806	Other disorders of bilirubin metabolism
E807	Disorder of bilirubin metabolism, unspecified
E8840	Mitochondrial metabolism disorder, unspecified
E8841	MELAS syndrome
E8842	MERRF syndrome
E8849	Other mitochondrial metabolism disorders
E8889	Other specified metabolic disorders
H49811	Kearns-Sayre syndrome, right eye
H49812	Kearns-Sayre syndrome, left eye
H49813	Kearns-Sayre syndrome, bilateral
H49819	Kearns-Sayre syndrome, unspecified eye

PDX Collection 3656
C965	Multifocal and unisystemic Langerhans-cell histiocytosis
C966	Unifocal Langerhans-cell histiocytosis
E71310	Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311	Medium chain acyl CoA dehydrogenase deficiency
E71312	Short chain acyl CoA dehydrogenase deficiency
E71313	Glutaric aciduria type II
E71314	Muscle carnitine palmitoyltransferase deficiency
E71318	Other disorders of fatty-acid oxidation
E7132	Disorders of ketone metabolism
E7139	Other disorders of fatty-acid metabolism
E7140	Disorder of carnitine metabolism, unspecified
E7141	Primary carnitine deficiency
E7142	Carnitine deficiency due to inborn errors of metabolism
E7143	Iatrogenic carnitine deficiency
E71440	Ruvalcaba-Myhre-Smith syndrome
E71448	Other secondary carnitine deficiency
E71518	Other disorders of peroxisome biogenesis
E803	Defects of catalase and peroxidase
E804	Gilbert syndrome
E805	Crigler-Najjar syndrome
E806	Other disorders of bilirubin metabolism
E807	Disorder of bilirubin metabolism, unspecified
E8840	Mitochondrial metabolism disorder, unspecified
E8841	MELAS syndrome
E8842	MERRF syndrome
E8849	Other mitochondrial metabolism disorders
E8889	Other specified metabolic disorders
H49811	Kearns-Sayre syndrome, right eye
H49812	Kearns-Sayre syndrome, left eye
H49813	Kearns-Sayre syndrome, bilateral
H49819	Kearns-Sayre syndrome, unspecified eye

PDX Collection 3658
C965	Multifocal and unisystemic Langerhans-cell histiocytosis
C966	Unifocal Langerhans-cell histiocytosis
E71310	Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311	Medium chain acyl CoA dehydrogenase deficiency
E71312	Short chain acyl CoA dehydrogenase deficiency
E71313	Glutaric aciduria type II
E71314	Muscle carnitine palmitoyltransferase deficiency
E71318	Other disorders of fatty-acid oxidation
E7132	Disorders of ketone metabolism
E7139	Other disorders of fatty-acid metabolism
E7140	Disorder of carnitine metabolism, unspecified
E7141	Primary carnitine deficiency
E7142	Carnitine deficiency due to inborn errors of metabolism
E7143	Iatrogenic carnitine deficiency
E71440	Ruvalcaba-Myhre-Smith syndrome
E71448	Other secondary carnitine deficiency
E71520	Childhood cerebral X-linked adrenoleukodystrophy
E803	Defects of catalase and peroxidase
E804	Gilbert syndrome
E805	Crigler-Najjar syndrome
E806	Other disorders of bilirubin metabolism
E807	Disorder of bilirubin metabolism, unspecified
E8840	Mitochondrial metabolism disorder, unspecified
E8841	MELAS syndrome
E8842	MERRF syndrome
E8849	Other mitochondrial metabolism disorders
E8889	Other specified metabolic disorders
H49811	Kearns-Sayre syndrome, right eye
H49812	Kearns-Sayre syndrome, left eye
H49813	Kearns-Sayre syndrome, bilateral
H49819	Kearns-Sayre syndrome, unspecified eye

PDX Collection 3660
C965	Multifocal and unisystemic Langerhans-cell histiocytosis
C966	Unifocal Langerhans-cell histiocytosis
E71310	Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311	Medium chain acyl CoA dehydrogenase deficiency
E71312	Short chain acyl CoA dehydrogenase deficiency
E71313	Glutaric aciduria type II
E71314	Muscle carnitine palmitoyltransferase deficiency
E71318	Other disorders of fatty-acid oxidation
E7132	Disorders of ketone metabolism
E7139	Other disorders of fatty-acid metabolism
E7140	Disorder of carnitine metabolism, unspecified
E7141	Primary carnitine deficiency
E7142	Carnitine deficiency due to inborn errors of metabolism
E7143	Iatrogenic carnitine deficiency
E71440	Ruvalcaba-Myhre-Smith syndrome
E71448	Other secondary carnitine deficiency
E71521	Adolescent X-linked adrenoleukodystrophy
E803	Defects of catalase and peroxidase
E804	Gilbert syndrome
E805	Crigler-Najjar syndrome
E806	Other disorders of bilirubin metabolism
E807	Disorder of bilirubin metabolism, unspecified
E8840	Mitochondrial metabolism disorder, unspecified
E8841	MELAS syndrome
E8842	MERRF syndrome
E8849	Other mitochondrial metabolism disorders
E8889	Other specified metabolic disorders
H49811	Kearns-Sayre syndrome, right eye
H49812	Kearns-Sayre syndrome, left eye
H49813	Kearns-Sayre syndrome, bilateral
H49819	Kearns-Sayre syndrome, unspecified eye

PDX Collection 3662
C965	Multifocal and unisystemic Langerhans-cell histiocytosis
C966	Unifocal Langerhans-cell histiocytosis
E71310	Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311	Medium chain acyl CoA dehydrogenase deficiency
E71312	Short chain acyl CoA dehydrogenase deficiency
E71313	Glutaric aciduria type II
E71314	Muscle carnitine palmitoyltransferase deficiency
E71318	Other disorders of fatty-acid oxidation
E7132	Disorders of ketone metabolism
E7139	Other disorders of fatty-acid metabolism
E7140	Disorder of carnitine metabolism, unspecified
E7141	Primary carnitine deficiency
E7142	Carnitine deficiency due to inborn errors of metabolism
E7143	Iatrogenic carnitine deficiency
E71440	Ruvalcaba-Myhre-Smith syndrome
E71448	Other secondary carnitine deficiency
E71522	Adrenomyeloneuropathy
E803	Defects of catalase and peroxidase
E804	Gilbert syndrome
E805	Crigler-Najjar syndrome
E806	Other disorders of bilirubin metabolism
E807	Disorder of bilirubin metabolism, unspecified
E8840	Mitochondrial metabolism disorder, unspecified
E8841	MELAS syndrome
E8842	MERRF syndrome
E8849	Other mitochondrial metabolism disorders
E8889	Other specified metabolic disorders
H49811	Kearns-Sayre syndrome, right eye
H49812	Kearns-Sayre syndrome, left eye
H49813	Kearns-Sayre syndrome, bilateral
H49819	Kearns-Sayre syndrome, unspecified eye

PDX Collection 3664
C965	Multifocal and unisystemic Langerhans-cell histiocytosis
C966	Unifocal Langerhans-cell histiocytosis
E71310	Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311	Medium chain acyl CoA dehydrogenase deficiency
E71312	Short chain acyl CoA dehydrogenase deficiency
E71313	Glutaric aciduria type II
E71314	Muscle carnitine palmitoyltransferase deficiency
E71318	Other disorders of fatty-acid oxidation
E7132	Disorders of ketone metabolism
E7139	Other disorders of fatty-acid metabolism
E7140	Disorder of carnitine metabolism, unspecified
E7141	Primary carnitine deficiency
E7142	Carnitine deficiency due to inborn errors of metabolism
E7143	Iatrogenic carnitine deficiency
E71440	Ruvalcaba-Myhre-Smith syndrome
E71448	Other secondary carnitine deficiency
E71528	Other X-linked adrenoleukodystrophy
E803	Defects of catalase and peroxidase
E804	Gilbert syndrome
E805	Crigler-Najjar syndrome
E806	Other disorders of bilirubin metabolism
E807	Disorder of bilirubin metabolism, unspecified
E8840	Mitochondrial metabolism disorder, unspecified
E8841	MELAS syndrome
E8842	MERRF syndrome
E8849	Other mitochondrial metabolism disorders
E8889	Other specified metabolic disorders
H49811	Kearns-Sayre syndrome, right eye
H49812	Kearns-Sayre syndrome, left eye
H49813	Kearns-Sayre syndrome, bilateral
H49819	Kearns-Sayre syndrome, unspecified eye

PDX Collection 3666
C965	Multifocal and unisystemic Langerhans-cell histiocytosis
C966	Unifocal Langerhans-cell histiocytosis
E71310	Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311	Medium chain acyl CoA dehydrogenase deficiency
E71312	Short chain acyl CoA dehydrogenase deficiency
E71313	Glutaric aciduria type II
E71314	Muscle carnitine palmitoyltransferase deficiency
E71318	Other disorders of fatty-acid oxidation
E7132	Disorders of ketone metabolism
E7139	Other disorders of fatty-acid metabolism
E7140	Disorder of carnitine metabolism, unspecified
E7141	Primary carnitine deficiency
E7142	Carnitine deficiency due to inborn errors of metabolism
E7143	Iatrogenic carnitine deficiency
E71440	Ruvalcaba-Myhre-Smith syndrome
E71448	Other secondary carnitine deficiency
E71529	X-linked adrenoleukodystrophy, unspecified type
E803	Defects of catalase and peroxidase
E804	Gilbert syndrome
E805	Crigler-Najjar syndrome
E806	Other disorders of bilirubin metabolism
E807	Disorder of bilirubin metabolism, unspecified
E8840	Mitochondrial metabolism disorder, unspecified
E8841	MELAS syndrome
E8842	MERRF syndrome
E8849	Other mitochondrial metabolism disorders
E8889	Other specified metabolic disorders
H49811	Kearns-Sayre syndrome, right eye
H49812	Kearns-Sayre syndrome, left eye
H49813	Kearns-Sayre syndrome, bilateral
H49819	Kearns-Sayre syndrome, unspecified eye

PDX Collection 3668
C965	Multifocal and unisystemic Langerhans-cell histiocytosis
C966	Unifocal Langerhans-cell histiocytosis
E71310	Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311	Medium chain acyl CoA dehydrogenase deficiency
E71312	Short chain acyl CoA dehydrogenase deficiency
E71313	Glutaric aciduria type II
E71314	Muscle carnitine palmitoyltransferase deficiency
E71318	Other disorders of fatty-acid oxidation
E7132	Disorders of ketone metabolism
E7139	Other disorders of fatty-acid metabolism
E7140	Disorder of carnitine metabolism, unspecified
E7141	Primary carnitine deficiency
E7142	Carnitine deficiency due to inborn errors of metabolism
E7143	Iatrogenic carnitine deficiency
E71440	Ruvalcaba-Myhre-Smith syndrome
E71448	Other secondary carnitine deficiency
E7153	Other group 2 peroxisomal disorders
E803	Defects of catalase and peroxidase
E804	Gilbert syndrome
E805	Crigler-Najjar syndrome
E806	Other disorders of bilirubin metabolism
E807	Disorder of bilirubin metabolism, unspecified
E8840	Mitochondrial metabolism disorder, unspecified
E8841	MELAS syndrome
E8842	MERRF syndrome
E8849	Other mitochondrial metabolism disorders
E8889	Other specified metabolic disorders
H49811	Kearns-Sayre syndrome, right eye
H49812	Kearns-Sayre syndrome, left eye
H49813	Kearns-Sayre syndrome, bilateral
H49819	Kearns-Sayre syndrome, unspecified eye

PDX Collection 3670
C965	Multifocal and unisystemic Langerhans-cell histiocytosis
C966	Unifocal Langerhans-cell histiocytosis
E71310	Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311	Medium chain acyl CoA dehydrogenase deficiency
E71312	Short chain acyl CoA dehydrogenase deficiency
E71313	Glutaric aciduria type II
E71314	Muscle carnitine palmitoyltransferase deficiency
E71318	Other disorders of fatty-acid oxidation
E7132	Disorders of ketone metabolism
E7139	Other disorders of fatty-acid metabolism
E7140	Disorder of carnitine metabolism, unspecified
E7141	Primary carnitine deficiency
E7142	Carnitine deficiency due to inborn errors of metabolism
E7143	Iatrogenic carnitine deficiency
E71440	Ruvalcaba-Myhre-Smith syndrome
E71448	Other secondary carnitine deficiency
E71540	Rhizomelic chondrodysplasia punctata
E803	Defects of catalase and peroxidase
E804	Gilbert syndrome
E805	Crigler-Najjar syndrome
E806	Other disorders of bilirubin metabolism
E807	Disorder of bilirubin metabolism, unspecified
E8840	Mitochondrial metabolism disorder, unspecified
E8841	MELAS syndrome
E8842	MERRF syndrome
E8849	Other mitochondrial metabolism disorders
E8889	Other specified metabolic disorders
H49811	Kearns-Sayre syndrome, right eye
H49812	Kearns-Sayre syndrome, left eye
H49813	Kearns-Sayre syndrome, bilateral
H49819	Kearns-Sayre syndrome, unspecified eye

PDX Collection 3672
C965	Multifocal and unisystemic Langerhans-cell histiocytosis
C966	Unifocal Langerhans-cell histiocytosis
E71310	Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311	Medium chain acyl CoA dehydrogenase deficiency
E71312	Short chain acyl CoA dehydrogenase deficiency
E71313	Glutaric aciduria type II
E71314	Muscle carnitine palmitoyltransferase deficiency
E71318	Other disorders of fatty-acid oxidation
E7132	Disorders of ketone metabolism
E7139	Other disorders of fatty-acid metabolism
E7140	Disorder of carnitine metabolism, unspecified
E7141	Primary carnitine deficiency
E7142	Carnitine deficiency due to inborn errors of metabolism
E7143	Iatrogenic carnitine deficiency
E71440	Ruvalcaba-Myhre-Smith syndrome
E71448	Other secondary carnitine deficiency
E71541	Zellweger-like syndrome
E803	Defects of catalase and peroxidase
E804	Gilbert syndrome
E805	Crigler-Najjar syndrome
E806	Other disorders of bilirubin metabolism
E807	Disorder of bilirubin metabolism, unspecified
E8840	Mitochondrial metabolism disorder, unspecified
E8841	MELAS syndrome
E8842	MERRF syndrome
E8849	Other mitochondrial metabolism disorders
E8889	Other specified metabolic disorders
H49811	Kearns-Sayre syndrome, right eye
H49812	Kearns-Sayre syndrome, left eye
H49813	Kearns-Sayre syndrome, bilateral
H49819	Kearns-Sayre syndrome, unspecified eye

PDX Collection 3674
C965	Multifocal and unisystemic Langerhans-cell histiocytosis
C966	Unifocal Langerhans-cell histiocytosis
E71310	Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311	Medium chain acyl CoA dehydrogenase deficiency
E71312	Short chain acyl CoA dehydrogenase deficiency
E71313	Glutaric aciduria type II
E71314	Muscle carnitine palmitoyltransferase deficiency
E71318	Other disorders of fatty-acid oxidation
E7132	Disorders of ketone metabolism
E7139	Other disorders of fatty-acid metabolism
E7140	Disorder of carnitine metabolism, unspecified
E7141	Primary carnitine deficiency

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