ICD-10-CM/PCS MS-DRG v40.0 Definitions Manual
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DRAFT
ICD-10-CM/PCS MS-DRG v40.0 Definitions Manual |
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| Appendix C: Principal diagnoses which convert CC/MCC to non-CC |
| Page 48 of 1270 |
| PDX Collection 0535 (continued) | |
| E8840 | Mitochondrial metabolism disorder, unspecified |
| E8841 | MELAS syndrome |
| E8842 | MERRF syndrome |
| E8849 | Other mitochondrial metabolism disorders |
| E8889 | Other specified metabolic disorders |
| H49811 | Kearns-Sayre syndrome, right eye |
| H49812 | Kearns-Sayre syndrome, left eye |
| H49813 | Kearns-Sayre syndrome, bilateral |
| H49819 | Kearns-Sayre syndrome, unspecified eye |
| PDX Collection 0536 | |
| C965 | Multifocal and unisystemic Langerhans-cell histiocytosis |
| C966 | Unifocal Langerhans-cell histiocytosis |
| E71310 | Long chain/very long chain acyl CoA dehydrogenase deficiency |
| E71311 | Medium chain acyl CoA dehydrogenase deficiency |
| E71312 | Short chain acyl CoA dehydrogenase deficiency |
| E71313 | Glutaric aciduria type II |
| E71314 | Muscle carnitine palmitoyltransferase deficiency |
| E71318 | Other disorders of fatty-acid oxidation |
| E7132 | Disorders of ketone metabolism |
| E7139 | Other disorders of fatty-acid metabolism |
| E7140 | Disorder of carnitine metabolism, unspecified |
| E7141 | Primary carnitine deficiency |
| E7142 | Carnitine deficiency due to inborn errors of metabolism |
| E7143 | Iatrogenic carnitine deficiency |
| E71440 | Ruvalcaba-Myhre-Smith syndrome |
| E71448 | Other secondary carnitine deficiency |
| E71548 | Other peroxisomal disorders |
| E803 | Defects of catalase and peroxidase |
| E804 | Gilbert syndrome |
| E805 | Crigler-Najjar syndrome |
| E806 | Other disorders of bilirubin metabolism |
| E807 | Disorder of bilirubin metabolism, unspecified |
| E8840 | Mitochondrial metabolism disorder, unspecified |
| E8841 | MELAS syndrome |
| E8842 | MERRF syndrome |
| E8849 | Other mitochondrial metabolism disorders |
| E8889 | Other specified metabolic disorders |
| H49811 | Kearns-Sayre syndrome, right eye |
| H49812 | Kearns-Sayre syndrome, left eye |
| H49813 | Kearns-Sayre syndrome, bilateral |
| H49819 | Kearns-Sayre syndrome, unspecified eye |
| PDX Collection 0537 | |
| E7500 | GM2 gangliosidosis, unspecified |
| E7501 | Sandhoff disease |
| E7502 | Tay-Sachs disease |
| E7509 | Other GM2 gangliosidosis |
| E7510 | Unspecified gangliosidosis |
| E7511 | Mucolipidosis IV |
| E7519 | Other gangliosidosis |
| E754 | Neuronal ceroid lipofuscinosis |
| F842 | Rett's syndrome |
| G132 | Systemic atrophy primarily affecting the central nervous system in myxedema |
| G138 | Systemic atrophy primarily affecting central nervous system in other diseases classified elsewhere |
| G300 | Alzheimer's disease with early onset |
| G301 | Alzheimer's disease with late onset |
| G308 | Other Alzheimer's disease |
| G309 | Alzheimer's disease, unspecified |
| G3101 | Pick's disease |
| G3109 | Other frontotemporal neurocognitive disorder |
| G311 | Senile degeneration of brain, not elsewhere classified |
| G312 | Degeneration of nervous system due to alcohol |
| G3181 | Alpers disease |
| G3182 | Leigh's disease |
| G3184 | Mild cognitive impairment of uncertain or unknown etiology |
| G3185 | Corticobasal degeneration |
| G3189 | Other specified degenerative diseases of nervous system |
| G319 | Degenerative disease of nervous system, unspecified |
| G914 | Hydrocephalus in diseases classified elsewhere |
| G94 | Other disorders of brain in diseases classified elsewhere |
| PDX Collection 0538 | |
| E7500 | GM2 gangliosidosis, unspecified |
| E7501 | Sandhoff disease |
| E7502 | Tay-Sachs disease |
| E7509 | Other GM2 gangliosidosis |
| E7510 | Unspecified gangliosidosis |
| E7511 | Mucolipidosis IV |
| E7519 | Other gangliosidosis |
| E7523 | Krabbe disease |
| E7525 | Metachromatic leukodystrophy |
| E7526 | Sulfatase deficiency |
| E7529 | Other sphingolipidosis |
| E754 | Neuronal ceroid lipofuscinosis |
| F842 | Rett's syndrome |
| G132 | Systemic atrophy primarily affecting the central nervous system in myxedema |
| G138 | Systemic atrophy primarily affecting central nervous system in other diseases classified elsewhere |
| G312 | Degeneration of nervous system due to alcohol |
| G3181 | Alpers disease |
| G3182 | Leigh's disease |
| G3289 | Other specified degenerative disorders of nervous system in diseases classified elsewhere |
| G914 | Hydrocephalus in diseases classified elsewhere |
| G9381 | Temporal sclerosis |
| G9389 | Other specified disorders of brain |
| G939 | Disorder of brain, unspecified |
| G94 | Other disorders of brain in diseases classified elsewhere |
| G969 | Disorder of central nervous system, unspecified |
| G980 | Neurogenic arthritis, not elsewhere classified |
| G988 | Other disorders of nervous system |
| G998 | Other specified disorders of nervous system in diseases classified elsewhere |
| PDX Collection 0539 | |
| D8130 | Adenosine deaminase deficiency, unspecified |
| D8131 | Severe combined immunodeficiency due to adenosine deaminase deficiency |
| D8132 | Adenosine deaminase 2 deficiency |
| D8139 | Other adenosine deaminase deficiency |
| D815 | Purine nucleoside phosphorylase [PNP] deficiency |
| D81810 | Biotinidase deficiency |
| D841 | Defects in the complement system |
| E7601 | Hurler's syndrome |
| E7602 | Hurler-Scheie syndrome |
| E7603 | Scheie's syndrome |
| E761 | Mucopolysaccharidosis, type II |
| E76210 | Morquio A mucopolysaccharidoses |
| E76211 | Morquio B mucopolysaccharidoses |
| E76219 | Morquio mucopolysaccharidoses, unspecified |
| E7622 | Sanfilippo mucopolysaccharidoses |
| E7629 | Other mucopolysaccharidoses |
| E763 | Mucopolysaccharidosis, unspecified |
| E768 | Other disorders of glucosaminoglycan metabolism |
| E769 | Glucosaminoglycan metabolism disorder, unspecified |
| E791 | Lesch-Nyhan syndrome |
| E792 | Myoadenylate deaminase deficiency |
| E798 | Other disorders of purine and pyrimidine metabolism |
| E799 | Disorder of purine and pyrimidine metabolism, unspecified |
| E800 | Hereditary erythropoietic porphyria |
| E801 | Porphyria cutanea tarda |
| E8020 | Unspecified porphyria |
| E8021 | Acute intermittent (hepatic) porphyria |
| E8029 | Other porphyria |
| E804 | Gilbert syndrome |
| E805 | Crigler-Najjar syndrome |
| E806 | Other disorders of bilirubin metabolism |
| E807 | Disorder of bilirubin metabolism, unspecified |
| E850 | Non-neuropathic heredofamilial amyloidosis |
| E859 | Amyloidosis, unspecified |
| E8881 | Metabolic syndrome |
| PDX Collection 0540 | |
| E7871 | Barth syndrome |
| E7872 | Smith-Lemli-Opitz syndrome |
| Q872 | Congenital malformation syndromes predominantly involving limbs |
| Q873 | Congenital malformation syndromes involving early overgrowth |
| Q8740 | Marfan's syndrome, unspecified |
| Q87410 | Marfan's syndrome with aortic dilation |
| Q87418 | Marfan's syndrome with other cardiovascular manifestations |
| Q8742 | Marfan's syndrome with ocular manifestations |
| Q8743 | Marfan's syndrome with skeletal manifestation |
| Q875 | Other congenital malformation syndromes with other skeletal changes |
| Q8781 | Alport syndrome |
| Q8782 | Arterial tortuosity syndrome |
| Q8789 | Other specified congenital malformation syndromes, not elsewhere classified |
| Q898 | Other specified congenital malformations |
| Q992 | Fragile X chromosome |
| PDX Collection 0541 | |
| E840 | Cystic fibrosis with pulmonary manifestations |
| E8411 | Meconium ileus in cystic fibrosis |
| E8419 | Cystic fibrosis with other intestinal manifestations |
| E848 | Cystic fibrosis with other manifestations |
| E849 | Cystic fibrosis, unspecified |
| PDX Collection 0542 | |
| E850 | Non-neuropathic heredofamilial amyloidosis |
| E851 | Neuropathic heredofamilial amyloidosis |
| E852 | Heredofamilial amyloidosis, unspecified |
| E853 | Secondary systemic amyloidosis |
| E854 | Organ-limited amyloidosis |
| E8581 | Light chain (AL) amyloidosis |
| E8582 | Wild-type transthyretin-related (ATTR) amyloidosis |
| E8589 | Other amyloidosis |
| E859 | Amyloidosis, unspecified |
| E8881 | Metabolic syndrome |
| PDX Collection 0545 | |
| C965 | Multifocal and unisystemic Langerhans-cell histiocytosis |
| C966 | Unifocal Langerhans-cell histiocytosis |
| E71310 | Long chain/very long chain acyl CoA dehydrogenase deficiency |
| E71311 | Medium chain acyl CoA dehydrogenase deficiency |
| E71312 | Short chain acyl CoA dehydrogenase deficiency |
| E71313 | Glutaric aciduria type II |
| E71314 | Muscle carnitine palmitoyltransferase deficiency |
| E71318 | Other disorders of fatty-acid oxidation |
| E7132 | Disorders of ketone metabolism |
| E7139 | Other disorders of fatty-acid metabolism |
| E7140 | Disorder of carnitine metabolism, unspecified |
| E7141 | Primary carnitine deficiency |
| E7142 | Carnitine deficiency due to inborn errors of metabolism |
| E7143 | Iatrogenic carnitine deficiency |
| E71440 | Ruvalcaba-Myhre-Smith syndrome |
| E71448 | Other secondary carnitine deficiency |
| E7150 | Peroxisomal disorder, unspecified |
| E71510 | Zellweger syndrome |
| E71511 | Neonatal adrenoleukodystrophy |
| E71518 | Other disorders of peroxisome biogenesis |
| E71520 | Childhood cerebral X-linked adrenoleukodystrophy |
| E71521 | Adolescent X-linked adrenoleukodystrophy |
| E71522 | Adrenomyeloneuropathy |
| E71528 | Other X-linked adrenoleukodystrophy |
| E71529 | X-linked adrenoleukodystrophy, unspecified type |
| E7153 | Other group 2 peroxisomal disorders |
| E71540 | Rhizomelic chondrodysplasia punctata |
| E71541 | Zellweger-like syndrome |
| E71542 | Other group 3 peroxisomal disorders |
| E71548 | Other peroxisomal disorders |
| E803 | Defects of catalase and peroxidase |
| E804 | Gilbert syndrome |
| E805 | Crigler-Najjar syndrome |
| E806 | Other disorders of bilirubin metabolism |
| E807 | Disorder of bilirubin metabolism, unspecified |
| E8889 | Other specified metabolic disorders |
| H49819 | Kearns-Sayre syndrome, unspecified eye |
| PDX Collection 0546 | |
| E368 | Other intraoperative complications of endocrine system |
| E89810 | Postprocedural hemorrhage of an endocrine system organ or structure following an endocrine system procedure |
| E89811 | Postprocedural hemorrhage of an endocrine system organ or structure following other procedure |
| E89820 | Postprocedural hematoma of an endocrine system organ or structure following an endocrine system procedure |
| E89821 | Postprocedural hematoma of an endocrine system organ or structure following other procedure |
| E89822 | Postprocedural seroma of an endocrine system organ or structure following an endocrine system procedure |
| E89823 | Postprocedural seroma of an endocrine system organ or structure following other procedure |
| E8989 | Other postprocedural endocrine and metabolic complications and disorders |
| H95811 | Postprocedural stenosis of right external ear canal |
| H95812 | Postprocedural stenosis of left external ear canal |
| H95813 | Postprocedural stenosis of external ear canal, bilateral |
| H95819 | Postprocedural stenosis of unspecified external ear canal |
| H9588 | Other intraoperative complications and disorders of the ear and mastoid process, not elsewhere classified |
| H9589 | Other postprocedural complications and disorders of the ear and mastoid process, not elsewhere classified |
| I973 | Postprocedural hypertension |
| M9689 | Other intraoperative and postprocedural complications and disorders of the musculoskeletal system |
| N981 | Hyperstimulation of ovaries |
| N982 | Complications of attempted introduction of fertilized ovum following in vitro fertilization |
| N983 | Complications of attempted introduction of embryo in embryo transfer |
| N988 | Other complications associated with artificial fertilization |
| N989 | Complication associated with artificial fertilization, unspecified |
| T8182XA | Emphysema (subcutaneous) resulting from a procedure, initial encounter |
| T8189XA | Other complications of procedures, not elsewhere classified, initial encounter |
| T819XXA | Unspecified complication of procedure, initial encounter |
| PDX Collection 0549 | |
| F05 | Delirium due to known physiological condition |
| R45851 | Suicidal ideations |
| PDX Collection 0553 | |
| F3113 | Bipolar disorder, current episode manic without psychotic features, severe |
| F312 | Bipolar disorder, current episode manic severe with psychotic features |
| F3163 | Bipolar disorder, current episode mixed, severe, without psychotic features |
| F3164 | Bipolar disorder, current episode mixed, severe, with psychotic features |
| PDX Collection 0554 | |
| F3113 | Bipolar disorder, current episode manic without psychotic features, severe |
| F312 | Bipolar disorder, current episode manic severe with psychotic features |
| F314 | Bipolar disorder, current episode depressed, severe, without psychotic features |
| F315 | Bipolar disorder, current episode depressed, severe, with psychotic features |
| F3163 | Bipolar disorder, current episode mixed, severe, without psychotic features |
| F3164 | Bipolar disorder, current episode mixed, severe, with psychotic features |
| PDX Collection 0556 | |
| F459 | Somatoform disorder, unspecified |
| F5000 | Anorexia nervosa, unspecified |
| F5001 | Anorexia nervosa, restricting type |
| F5002 | Anorexia nervosa, binge eating/purging type |
| F502 | Bulimia nervosa |
| F5081 | Binge eating disorder |
| F5082 | Avoidant/restrictive food intake disorder |
| F5089 | Other specified eating disorder |
| F509 | Eating disorder, unspecified |
| F59 | Unspecified behavioral syndromes associated with physiological disturbances and physical factors |
| F9821 | Rumination disorder of infancy |
| F9829 | Other feeding disorders of infancy and early childhood |
| F983 | Pica of infancy and childhood |
| PDX Collection 0557 | |
| F5000 | Anorexia nervosa, unspecified |
| F5001 | Anorexia nervosa, restricting type |
| F5002 | Anorexia nervosa, binge eating/purging type |
| F502 | Bulimia nervosa |
| F5081 | Binge eating disorder |
| F5082 | Avoidant/restrictive food intake disorder |
| F5089 | Other specified eating disorder |
| F509 | Eating disorder, unspecified |
| F9821 | Rumination disorder of infancy |
| F9829 | Other feeding disorders of infancy and early childhood |
| PDX Collection 0558 | |
| F72 | Severe intellectual disabilities |
| F73 | Profound intellectual disabilities |
| PDX Collection 0559 | |
| A0221 | Salmonella meningitis |
| A170 | Tuberculous meningitis |
| A171 | Meningeal tuberculoma |
| A2781 | Aseptic meningitis in leptospirosis |
| A390 | Meningococcal meningitis |
| A5041 | Late congenital syphilitic meningitis |
| A5141 | Secondary syphilitic meningitis |
| A5213 | Late syphilitic meningitis |
| A5482 | Gonococcal brain abscess |
| A5484 | Gonococcal pneumonia |
| A5489 | Other gonococcal infections |
| A549 | Gonococcal infection, unspecified |
| A870 | Enteroviral meningitis |
| A871 | Adenoviral meningitis |
| A872 | Lymphocytic choriomeningitis |
| A878 | Other viral meningitis |
| A879 | Viral meningitis, unspecified |
| B003 | Herpesviral meningitis |
| B021 | Zoster meningitis |
| B261 | Mumps meningitis |
| B375 | Candidal meningitis |
| B384 | Coccidioidomycosis meningitis |
| B451 | Cerebral cryptococcosis |
| B582 | Toxoplasma meningoencephalitis |
| G000 | Hemophilus meningitis |
| G001 | Pneumococcal meningitis |
| G002 | Streptococcal meningitis |
| G003 | Staphylococcal meningitis |
| G008 | Other bacterial meningitis |
| G009 | Bacterial meningitis, unspecified |
| G01 | Meningitis in bacterial diseases classified elsewhere |
| G02 | Meningitis in other infectious and parasitic diseases classified elsewhere |
| G030 | Nonpyogenic meningitis |
| G031 | Chronic meningitis |
| G032 | Benign recurrent meningitis [Mollaret] |
| G038 | Meningitis due to other specified causes |
| G039 | Meningitis, unspecified |
| G042 | Bacterial meningoencephalitis and meningomyelitis, not elsewhere classified |
| G3289 | Other specified degenerative disorders of nervous system in diseases classified elsewhere |
| G610 | Guillain-Barre syndrome |
| G969 | Disorder of central nervous system, unspecified |
| G980 | Neurogenic arthritis, not elsewhere classified |
| G988 | Other disorders of nervous system |
| G998 | Other specified disorders of nervous system in diseases classified elsewhere |
| PDX Collection 0560 | |
| A0221 | Salmonella meningitis |
| A170 | Tuberculous meningitis |
| A171 | Meningeal tuberculoma |
| A1782 | Tuberculous meningoencephalitis |
| A2781 | Aseptic meningitis in leptospirosis |
| A390 | Meningococcal meningitis |
| A5041 | Late congenital syphilitic meningitis |
| A5042 | Late congenital syphilitic encephalitis |
| A5141 | Secondary syphilitic meningitis |
| A5213 | Late syphilitic meningitis |
| A5214 | Late syphilitic encephalitis |
| A5482 | Gonococcal brain abscess |
| A5484 | Gonococcal pneumonia |
| A5489 | Other gonococcal infections |
| A549 | Gonococcal infection, unspecified |
| A811 | Subacute sclerosing panencephalitis |
| A8182 | Gerstmann-Straussler-Scheinker syndrome |
| A8183 | Fatal familial insomnia |
| A8189 | Other atypical virus infections of central nervous system |
| A830 | Japanese encephalitis |
| A831 | Western equine encephalitis |
| A832 | Eastern equine encephalitis |
| A833 | St Louis encephalitis |
| A834 | Australian encephalitis |
| A835 | California encephalitis |
| A836 | Rocio virus disease |
| A838 | Other mosquito-borne viral encephalitis |
| A839 | Mosquito-borne viral encephalitis, unspecified |
| A840 | Far Eastern tick-borne encephalitis [Russian spring-summer encephalitis] |
| A841 | Central European tick-borne encephalitis |
| A8481 | Powassan virus disease |
| A8489 | Other tick-borne viral encephalitis |
| A849 | Tick-borne viral encephalitis, unspecified |
| A850 | Enteroviral encephalitis |
| A851 | Adenoviral encephalitis |
| A852 | Arthropod-borne viral encephalitis, unspecified |
| A858 | Other specified viral encephalitis |
| A870 | Enteroviral meningitis |
| A871 | Adenoviral meningitis |
| A872 | Lymphocytic choriomeningitis |
| A878 | Other viral meningitis |
| A879 | Viral meningitis, unspecified |
| A880 | Enteroviral exanthematous fever [Boston exanthem] |
| A888 | Other specified viral infections of central nervous system |
| A921 | O'nyong-nyong fever |
| A922 | Venezuelan equine fever |
| A9230 | West Nile virus infection, unspecified |
| A9231 | West Nile virus infection with encephalitis |
| A9232 | West Nile virus infection with other neurologic manifestation |
| A9239 | West Nile virus infection with other complications |
| A924 | Rift Valley fever |
| A925 | Zika virus disease |
| A928 | Other specified mosquito-borne viral fevers |
| A930 | Oropouche virus disease |
| A962 | Lassa fever |
| A983 | Marburg virus disease |
| A984 | Ebola virus disease |
| B003 | Herpesviral meningitis |
| B004 | Herpesviral encephalitis |
| B0089 | Other herpesviral infection |
| B009 | Herpesviral infection, unspecified |
| B010 | Varicella meningitis |
| B0111 | Varicella encephalitis and encephalomyelitis |
| B0181 | Varicella keratitis |
| B0189 | Other varicella complications |
| B019 | Varicella without complication |
| B020 | Zoster encephalitis |
| B021 | Zoster meningitis |
| B0221 | Postherpetic geniculate ganglionitis |
| B0222 | Postherpetic trigeminal neuralgia |
| B0223 | Postherpetic polyneuropathy |
| B0229 | Other postherpetic nervous system involvement |
| B027 | Disseminated zoster |
| B028 | Zoster with other complications |
| B029 | Zoster without complications |
| B04 | Monkeypox |
| B0601 | Rubella encephalitis |
| B0804 | Paravaccinia, unspecified |
| B0809 | Other orthopoxvirus infections |
| B0820 | Exanthema subitum [sixth disease], unspecified |
| B0821 | Exanthema subitum [sixth disease] due to human herpesvirus 6 |
| B0822 | Exanthema subitum [sixth disease] due to human herpesvirus 7 |
| B0860 | Parapoxvirus infection, unspecified |
| B0861 | Bovine stomatitis |
| B0862 | Sealpox |
| B0869 | Other parapoxvirus infections |
| B0870 | Yatapoxvirus infection, unspecified |
| B0871 | Tanapox virus disease |
| B0872 | Yaba pox virus disease |
| B0879 | Other yatapoxvirus infections |
| B09 | Unspecified viral infection characterized by skin and mucous membrane lesions |
| B1001 | Human herpesvirus 6 encephalitis |
| B1009 | Other human herpesvirus encephalitis |
| B1081 | Human herpesvirus 6 infection |
| B1082 | Human herpesvirus 7 infection |
| B1089 | Other human herpesvirus infection |
| B261 | Mumps meningitis |
| B262 | Mumps encephalitis |
| B2700 | Gammaherpesviral mononucleosis without complication |
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Centers for Medicare & Medicaid Services, 7500 Security Boulevard Baltimore, MD 21244 16 Mar 2022 17:08:13 CMS, code-revision=333, description-revision=1331 |