ICD-10-CM/PCS MS-DRG v40.0 Definitions Manual
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DRAFT
ICD-10-CM/PCS MS-DRG v40.0 Definitions Manual |
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| Appendix G: Diagnoses Defined as Complications or Comorbidities |
| Page 4 of 37 |
| A000 B083 C7240 C84Z1 E7200 F3181 H4742 I75023 K51012 L97518 M4858XA M84512P M87032 N983 O98312 S0211HA S12390A S32111A S42036P S42432K S52031K S52256N S52392R S58011A S62222P S62613K S72031K S72331R S72462R S82026P S82201M S82441Q S82873P S92046P S92513K T333XXA T83512A |
| C84Z1 | Other mature T/NK-cell lymphomas, lymph nodes of head, face, and neck |
| C84Z2 | Other mature T/NK-cell lymphomas, intrathoracic lymph nodes |
| C84Z3 | Other mature T/NK-cell lymphomas, intra-abdominal lymph nodes |
| C84Z4 | Other mature T/NK-cell lymphomas, lymph nodes of axilla and upper limb |
| C84Z5 | Other mature T/NK-cell lymphomas, lymph nodes of inguinal region and lower limb |
| C84Z6 | Other mature T/NK-cell lymphomas, intrapelvic lymph nodes |
| C84Z7 | Other mature T/NK-cell lymphomas, spleen |
| C84Z8 | Other mature T/NK-cell lymphomas, lymph nodes of multiple sites |
| C84Z9 | Other mature T/NK-cell lymphomas, extranodal and solid organ sites |
| C8510 | Unspecified B-cell lymphoma, unspecified site |
| C8511 | Unspecified B-cell lymphoma, lymph nodes of head, face, and neck |
| C8512 | Unspecified B-cell lymphoma, intrathoracic lymph nodes |
| C8513 | Unspecified B-cell lymphoma, intra-abdominal lymph nodes |
| C8514 | Unspecified B-cell lymphoma, lymph nodes of axilla and upper limb |
| C8515 | Unspecified B-cell lymphoma, lymph nodes of inguinal region and lower limb |
| C8516 | Unspecified B-cell lymphoma, intrapelvic lymph nodes |
| C8517 | Unspecified B-cell lymphoma, spleen |
| C8518 | Unspecified B-cell lymphoma, lymph nodes of multiple sites |
| C8519 | Unspecified B-cell lymphoma, extranodal and solid organ sites |
| C8520 | Mediastinal (thymic) large B-cell lymphoma, unspecified site |
| C8521 | Mediastinal (thymic) large B-cell lymphoma, lymph nodes of head, face, and neck |
| C8522 | Mediastinal (thymic) large B-cell lymphoma, intrathoracic lymph nodes |
| C8523 | Mediastinal (thymic) large B-cell lymphoma, intra-abdominal lymph nodes |
| C8524 | Mediastinal (thymic) large B-cell lymphoma, lymph nodes of axilla and upper limb |
| C8525 | Mediastinal (thymic) large B-cell lymphoma, lymph nodes of inguinal region and lower limb |
| C8526 | Mediastinal (thymic) large B-cell lymphoma, intrapelvic lymph nodes |
| C8527 | Mediastinal (thymic) large B-cell lymphoma, spleen |
| C8528 | Mediastinal (thymic) large B-cell lymphoma, lymph nodes of multiple sites |
| C8529 | Mediastinal (thymic) large B-cell lymphoma, extranodal and solid organ sites |
| C8580 | Other specified types of non-Hodgkin lymphoma, unspecified site |
| C8581 | Other specified types of non-Hodgkin lymphoma, lymph nodes of head, face, and neck |
| C8582 | Other specified types of non-Hodgkin lymphoma, intrathoracic lymph nodes |
| C8583 | Other specified types of non-Hodgkin lymphoma, intra-abdominal lymph nodes |
| C8584 | Other specified types of non-Hodgkin lymphoma, lymph nodes of axilla and upper limb |
| C8585 | Other specified types of non-Hodgkin lymphoma, lymph nodes of inguinal region and lower limb |
| C8586 | Other specified types of non-Hodgkin lymphoma, intrapelvic lymph nodes |
| C8587 | Other specified types of non-Hodgkin lymphoma, spleen |
| C8588 | Other specified types of non-Hodgkin lymphoma, lymph nodes of multiple sites |
| C8589 | Other specified types of non-Hodgkin lymphoma, extranodal and solid organ sites |
| C8590 | Non-Hodgkin lymphoma, unspecified, unspecified site |
| C8591 | Non-Hodgkin lymphoma, unspecified, lymph nodes of head, face, and neck |
| C8592 | Non-Hodgkin lymphoma, unspecified, intrathoracic lymph nodes |
| C8593 | Non-Hodgkin lymphoma, unspecified, intra-abdominal lymph nodes |
| C8594 | Non-Hodgkin lymphoma, unspecified, lymph nodes of axilla and upper limb |
| C8595 | Non-Hodgkin lymphoma, unspecified, lymph nodes of inguinal region and lower limb |
| C8596 | Non-Hodgkin lymphoma, unspecified, intrapelvic lymph nodes |
| C8597 | Non-Hodgkin lymphoma, unspecified, spleen |
| C8598 | Non-Hodgkin lymphoma, unspecified, lymph nodes of multiple sites |
| C8599 | Non-Hodgkin lymphoma, unspecified, extranodal and solid organ sites |
| C860 | Extranodal NK/T-cell lymphoma, nasal type |
| C861 | Hepatosplenic T-cell lymphoma |
| C862 | Enteropathy-type (intestinal) T-cell lymphoma |
| C863 | Subcutaneous panniculitis-like T-cell lymphoma |
| C864 | Blastic NK-cell lymphoma |
| C865 | Angioimmunoblastic T-cell lymphoma |
| C866 | Primary cutaneous CD30-positive T-cell proliferations |
| C882 | Heavy chain disease |
| C883 | Immunoproliferative small intestinal disease |
| C884 | Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] |
| C888 | Other malignant immunoproliferative diseases |
| C889 | Malignant immunoproliferative disease, unspecified |
| C9000 | Multiple myeloma not having achieved remission |
| C9001 | Multiple myeloma in remission |
| C9002 | Multiple myeloma in relapse |
| C9010 | Plasma cell leukemia not having achieved remission |
| C9011 | Plasma cell leukemia in remission |
| C9012 | Plasma cell leukemia in relapse |
| C9020 | Extramedullary plasmacytoma not having achieved remission |
| C9021 | Extramedullary plasmacytoma in remission |
| C9022 | Extramedullary plasmacytoma in relapse |
| C9030 | Solitary plasmacytoma not having achieved remission |
| C9031 | Solitary plasmacytoma in remission |
| C9032 | Solitary plasmacytoma in relapse |
| C9100 | Acute lymphoblastic leukemia not having achieved remission |
| C9101 | Acute lymphoblastic leukemia, in remission |
| C9102 | Acute lymphoblastic leukemia, in relapse |
| C9110 | Chronic lymphocytic leukemia of B-cell type not having achieved remission |
| C9111 | Chronic lymphocytic leukemia of B-cell type in remission |
| C9112 | Chronic lymphocytic leukemia of B-cell type in relapse |
| C9130 | Prolymphocytic leukemia of B-cell type not having achieved remission |
| C9131 | Prolymphocytic leukemia of B-cell type, in remission |
| C9132 | Prolymphocytic leukemia of B-cell type, in relapse |
| C9140 | Hairy cell leukemia not having achieved remission |
| C9141 | Hairy cell leukemia, in remission |
| C9142 | Hairy cell leukemia, in relapse |
| C9150 | Adult T-cell lymphoma/leukemia (HTLV-1-associated) not having achieved remission |
| C9151 | Adult T-cell lymphoma/leukemia (HTLV-1-associated), in remission |
| C9152 | Adult T-cell lymphoma/leukemia (HTLV-1-associated), in relapse |
| C9160 | Prolymphocytic leukemia of T-cell type not having achieved remission |
| C9161 | Prolymphocytic leukemia of T-cell type, in remission |
| C9162 | Prolymphocytic leukemia of T-cell type, in relapse |
| C9190 | Lymphoid leukemia, unspecified not having achieved remission |
| C9191 | Lymphoid leukemia, unspecified, in remission |
| C9192 | Lymphoid leukemia, unspecified, in relapse |
| C91A0 | Mature B-cell leukemia Burkitt-type not having achieved remission |
| C91A1 | Mature B-cell leukemia Burkitt-type, in remission |
| C91A2 | Mature B-cell leukemia Burkitt-type, in relapse |
| C91Z0 | Other lymphoid leukemia not having achieved remission |
| C91Z1 | Other lymphoid leukemia, in remission |
| C91Z2 | Other lymphoid leukemia, in relapse |
| C9200 | Acute myeloblastic leukemia, not having achieved remission |
| C9201 | Acute myeloblastic leukemia, in remission |
| C9202 | Acute myeloblastic leukemia, in relapse |
| C9210 | Chronic myeloid leukemia, BCR/ABL-positive, not having achieved remission |
| C9211 | Chronic myeloid leukemia, BCR/ABL-positive, in remission |
| C9212 | Chronic myeloid leukemia, BCR/ABL-positive, in relapse |
| C9220 | Atypical chronic myeloid leukemia, BCR/ABL-negative, not having achieved remission |
| C9221 | Atypical chronic myeloid leukemia, BCR/ABL-negative, in remission |
| C9222 | Atypical chronic myeloid leukemia, BCR/ABL-negative, in relapse |
| C9230 | Myeloid sarcoma, not having achieved remission |
| C9231 | Myeloid sarcoma, in remission |
| C9232 | Myeloid sarcoma, in relapse |
| C9240 | Acute promyelocytic leukemia, not having achieved remission |
| C9241 | Acute promyelocytic leukemia, in remission |
| C9242 | Acute promyelocytic leukemia, in relapse |
| C9250 | Acute myelomonocytic leukemia, not having achieved remission |
| C9251 | Acute myelomonocytic leukemia, in remission |
| C9252 | Acute myelomonocytic leukemia, in relapse |
| C9260 | Acute myeloid leukemia with 11q23-abnormality not having achieved remission |
| C9261 | Acute myeloid leukemia with 11q23-abnormality in remission |
| C9262 | Acute myeloid leukemia with 11q23-abnormality in relapse |
| C9290 | Myeloid leukemia, unspecified, not having achieved remission |
| C9291 | Myeloid leukemia, unspecified in remission |
| C9292 | Myeloid leukemia, unspecified in relapse |
| C92A0 | Acute myeloid leukemia with multilineage dysplasia, not having achieved remission |
| C92A1 | Acute myeloid leukemia with multilineage dysplasia, in remission |
| C92A2 | Acute myeloid leukemia with multilineage dysplasia, in relapse |
| C92Z0 | Other myeloid leukemia not having achieved remission |
| C92Z1 | Other myeloid leukemia, in remission |
| C92Z2 | Other myeloid leukemia, in relapse |
| C9300 | Acute monoblastic/monocytic leukemia, not having achieved remission |
| C9301 | Acute monoblastic/monocytic leukemia, in remission |
| C9302 | Acute monoblastic/monocytic leukemia, in relapse |
| C9310 | Chronic myelomonocytic leukemia not having achieved remission |
| C9311 | Chronic myelomonocytic leukemia, in remission |
| C9312 | Chronic myelomonocytic leukemia, in relapse |
| C9330 | Juvenile myelomonocytic leukemia, not having achieved remission |
| C9331 | Juvenile myelomonocytic leukemia, in remission |
| C9332 | Juvenile myelomonocytic leukemia, in relapse |
| C9390 | Monocytic leukemia, unspecified, not having achieved remission |
| C9391 | Monocytic leukemia, unspecified in remission |
| C9392 | Monocytic leukemia, unspecified in relapse |
| C93Z0 | Other monocytic leukemia, not having achieved remission |
| C93Z1 | Other monocytic leukemia, in remission |
| C93Z2 | Other monocytic leukemia, in relapse |
| C9400 | Acute erythroid leukemia, not having achieved remission |
| C9401 | Acute erythroid leukemia, in remission |
| C9402 | Acute erythroid leukemia, in relapse |
| C9420 | Acute megakaryoblastic leukemia not having achieved remission |
| C9421 | Acute megakaryoblastic leukemia, in remission |
| C9422 | Acute megakaryoblastic leukemia, in relapse |
| C9430 | Mast cell leukemia not having achieved remission |
| C9431 | Mast cell leukemia, in remission |
| C9432 | Mast cell leukemia, in relapse |
| C9440 | Acute panmyelosis with myelofibrosis not having achieved remission |
| C9441 | Acute panmyelosis with myelofibrosis, in remission |
| C9442 | Acute panmyelosis with myelofibrosis, in relapse |
| C946 | Myelodysplastic disease, not elsewhere classified |
| C9480 | Other specified leukemias not having achieved remission |
| C9481 | Other specified leukemias, in remission |
| C9482 | Other specified leukemias, in relapse |
| C9500 | Acute leukemia of unspecified cell type not having achieved remission |
| C9501 | Acute leukemia of unspecified cell type, in remission |
| C9502 | Acute leukemia of unspecified cell type, in relapse |
| C9510 | Chronic leukemia of unspecified cell type not having achieved remission |
| C9511 | Chronic leukemia of unspecified cell type, in remission |
| C9512 | Chronic leukemia of unspecified cell type, in relapse |
| C9590 | Leukemia, unspecified not having achieved remission |
| C9591 | Leukemia, unspecified, in remission |
| C9592 | Leukemia, unspecified, in relapse |
| C960 | Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis |
| C9620 | Malignant mast cell neoplasm, unspecified |
| C9621 | Aggressive systemic mastocytosis |
| C9622 | Mast cell sarcoma |
| C9629 | Other malignant mast cell neoplasm |
| C964 | Sarcoma of dendritic cells (accessory cells) |
| C965 | Multifocal and unisystemic Langerhans-cell histiocytosis |
| C966 | Unifocal Langerhans-cell histiocytosis |
| C969 | Malignant neoplasm of lymphoid, hematopoietic and related tissue, unspecified |
| C96A | Histiocytic sarcoma |
| C96Z | Other specified malignant neoplasms of lymphoid, hematopoietic and related tissue |
| D4622 | Refractory anemia with excess of blasts 2 |
| D46C | Myelodysplastic syndrome with isolated del(5q) chromosomal abnormality |
| D4701 | Cutaneous mastocytosis |
| D4702 | Systemic mastocytosis |
| D4709 | Other mast cell neoplasms of uncertain behavior |
| D471 | Chronic myeloproliferative disease |
| D479 | Neoplasm of uncertain behavior of lymphoid, hematopoietic and related tissue, unspecified |
| D47Z1 | Post-transplant lymphoproliferative disorder (PTLD) |
| D47Z2 | Castleman disease |
| D47Z9 | Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue |
| D588 | Other specified hereditary hemolytic anemias |
| D589 | Hereditary hemolytic anemia, unspecified |
| D590 | Drug-induced autoimmune hemolytic anemia |
| D5910 | Autoimmune hemolytic anemia, unspecified |
| D5911 | Warm autoimmune hemolytic anemia |
| D5912 | Cold autoimmune hemolytic anemia |
| D5913 | Mixed type autoimmune hemolytic anemia |
| D5919 | Other autoimmune hemolytic anemia |
| D592 | Drug-induced nonautoimmune hemolytic anemia |
| D594 | Other nonautoimmune hemolytic anemias |
| D599 | Acquired hemolytic anemia, unspecified |
| D6101 | Constitutional (pure) red blood cell aplasia |
| D6109 | Other constitutional aplastic anemia |
| D61818 | Other pancytopenia |
| D6182 | Myelophthisis |
| D619 | Aplastic anemia, unspecified |
| D62 | Acute posthemorrhagic anemia |
| D6800 | Von Willebrand disease, unspecified |
| D6801 | Von Willebrand disease, type 1 |
| D68020 | Von Willebrand disease, type 2A |
| D68021 | Von Willebrand disease, type 2B |
| D68022 | Von Willebrand disease, type 2M |
| D68023 | Von Willebrand disease, type 2N |
| D68029 | Von Willebrand disease, type 2, unspecified |
| D6803 | Von Willebrand disease, type 3 |
| D6804 | Acquired von Willebrand disease |
| D6809 | Other von Willebrand disease |
| D681 | Hereditary factor XI deficiency |
| D682 | Hereditary deficiency of other clotting factors |
| D68311 | Acquired hemophilia |
| D68312 | Antiphospholipid antibody with hemorrhagic disorder |
| D68318 | Other hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors |
| D6832 | Hemorrhagic disorder due to extrinsic circulating anticoagulants |
| D684 | Acquired coagulation factor deficiency |
| D6851 | Activated protein C resistance |
| D6852 | Prothrombin gene mutation |
| D6859 | Other primary thrombophilia |
| D6861 | Antiphospholipid syndrome |
| D6862 | Lupus anticoagulant syndrome |
| D6869 | Other thrombophilia |
| D688 | Other specified coagulation defects |
| D689 | Coagulation defect, unspecified |
| D690 | Allergic purpura |
| D693 | Immune thrombocytopenic purpura |
| D6941 | Evans syndrome |
| D6942 | Congenital and hereditary thrombocytopenia purpura |
| D740 | Congenital methemoglobinemia |
| D748 | Other methemoglobinemias |
| D749 | Methemoglobinemia, unspecified |
| D7581 | Myelofibrosis |
| D761 | Hemophagocytic lymphohistiocytosis |
| D762 | Hemophagocytic syndrome, infection-associated |
| D763 | Other histiocytosis syndromes |
| D7801 | Intraoperative hemorrhage and hematoma of the spleen complicating a procedure on the spleen |
| D7802 | Intraoperative hemorrhage and hematoma of the spleen complicating other procedure |
| D7811 | Accidental puncture and laceration of the spleen during a procedure on the spleen |
| D7812 | Accidental puncture and laceration of the spleen during other procedure |
| D7821 | Postprocedural hemorrhage of the spleen following a procedure on the spleen |
| D7822 | Postprocedural hemorrhage of the spleen following other procedure |
| D7831 | Postprocedural hematoma of the spleen following a procedure on the spleen |
| D7832 | Postprocedural hematoma of the spleen following other procedure |
| D7833 | Postprocedural seroma of the spleen following a procedure on the spleen |
| D7834 | Postprocedural seroma of the spleen following other procedure |
| D7881 | Other intraoperative complications of the spleen |
| D7889 | Other postprocedural complications of the spleen |
| D800 | Hereditary hypogammaglobulinemia |
| D801 | Nonfamilial hypogammaglobulinemia |
| D802 | Selective deficiency of immunoglobulin A [IgA] |
| D803 | Selective deficiency of immunoglobulin G [IgG] subclasses |
| D804 | Selective deficiency of immunoglobulin M [IgM] |
| D805 | Immunodeficiency with increased immunoglobulin M [IgM] |
| D806 | Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia |
| D807 | Transient hypogammaglobulinemia of infancy |
| D808 | Other immunodeficiencies with predominantly antibody defects |
| D809 | Immunodeficiency with predominantly antibody defects, unspecified |
| D810 | Severe combined immunodeficiency [SCID] with reticular dysgenesis |
| D811 | Severe combined immunodeficiency [SCID] with low T- and B-cell numbers |
| D812 | Severe combined immunodeficiency [SCID] with low or normal B-cell numbers |
| D8130 | Adenosine deaminase deficiency, unspecified |
| D8131 | Severe combined immunodeficiency due to adenosine deaminase deficiency |
| D8132 | Adenosine deaminase 2 deficiency |
| D8139 | Other adenosine deaminase deficiency |
| D814 | Nezelof's syndrome |
| D815 | Purine nucleoside phosphorylase [PNP] deficiency |
| D816 | Major histocompatibility complex class I deficiency |
| D817 | Major histocompatibility complex class II deficiency |
| D8182 | Activated Phosphoinositide 3-kinase Delta Syndrome [APDS] |
| D8189 | Other combined immunodeficiencies |
| D819 | Combined immunodeficiency, unspecified |
| D820 | Wiskott-Aldrich syndrome |
| D821 | Di George's syndrome |
| D830 | Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function |
| D831 | Common variable immunodeficiency with predominant immunoregulatory T-cell disorders |
| D832 | Common variable immunodeficiency with autoantibodies to B- or T-cells |
| D838 | Other common variable immunodeficiencies |
| D839 | Common variable immunodeficiency, unspecified |
| D8481 | Immunodeficiency due to conditions classified elsewhere |
| D84821 | Immunodeficiency due to drugs |
| D84822 | Immunodeficiency due to external causes |
| D8489 | Other immunodeficiencies |
| D849 | Immunodeficiency, unspecified |
| D89810 | Acute graft-versus-host disease |
| D89811 | Chronic graft-versus-host disease |
| D89812 | Acute on chronic graft-versus-host disease |
| D89813 | Graft-versus-host disease, unspecified |
| D89833 | Cytokine release syndrome, grade 3 |
| D89834 | Cytokine release syndrome, grade 4 |
| D89835 | Cytokine release syndrome, grade 5 |
| E060 | Acute thyroiditis |
| E0852 | Diabetes mellitus due to underlying condition with diabetic peripheral angiopathy with gangrene |
| E0952 | Drug or chemical induced diabetes mellitus with diabetic peripheral angiopathy with gangrene |
| E1052 | Type 1 diabetes mellitus with diabetic peripheral angiopathy with gangrene |
| E1152 | Type 2 diabetes mellitus with diabetic peripheral angiopathy with gangrene |
| E1352 | Other specified diabetes mellitus with diabetic peripheral angiopathy with gangrene |
| E15 | Nondiabetic hypoglycemic coma |
| E221 | Hyperprolactinemia |
| E222 | Syndrome of inappropriate secretion of antidiuretic hormone |
| E228 | Other hyperfunction of pituitary gland |
| E229 | Hyperfunction of pituitary gland, unspecified |
| E230 | Hypopituitarism |
| E232 | Diabetes insipidus |
| E240 | Pituitary-dependent Cushing's disease |
| E242 | Drug-induced Cushing's syndrome |
| E243 | Ectopic ACTH syndrome |
| E244 | Alcohol-induced pseudo-Cushing's syndrome |
| E248 | Other Cushing's syndrome |
| E249 | Cushing's syndrome, unspecified |
| E270 | Other adrenocortical overactivity |
| E271 | Primary adrenocortical insufficiency |
| E272 | Addisonian crisis |
| E273 | Drug-induced adrenocortical insufficiency |
| E2740 | Unspecified adrenocortical insufficiency |
| E2749 | Other adrenocortical insufficiency |
| E275 | Adrenomedullary hyperfunction |
| E321 | Abscess of thymus |
| E340 | Carcinoid syndrome |
| E3601 | Intraoperative hemorrhage and hematoma of an endocrine system organ or structure complicating an endocrine system procedure |
| E3602 | Intraoperative hemorrhage and hematoma of an endocrine system organ or structure complicating other procedure |
| E3611 | Accidental puncture and laceration of an endocrine system organ or structure during an endocrine system procedure |
| E3612 | Accidental puncture and laceration of an endocrine system organ or structure during other procedure |
| E440 | Moderate protein-calorie malnutrition |
| E441 | Mild protein-calorie malnutrition |
| E45 | Retarded development following protein-calorie malnutrition |
| E46 | Unspecified protein-calorie malnutrition |
| E5111 | Dry beriberi |
| E5112 | Wet beriberi |
| E512 | Wernicke's encephalopathy |
| E518 | Other manifestations of thiamine deficiency |
| E519 | Thiamine deficiency, unspecified |
| E530 | Riboflavin deficiency |
| E550 | Rickets, active |
| E640 | Sequelae of protein-calorie malnutrition |
| E662 | Morbid (severe) obesity with alveolar hypoventilation |
| E700 | Classical phenylketonuria |
| E701 | Other hyperphenylalaninemias |
| E7020 | Disorder of tyrosine metabolism, unspecified |
| E7021 | Tyrosinemia |
| E7029 | Other disorders of tyrosine metabolism |
| E7030 | Albinism, unspecified |
| E70310 | X-linked ocular albinism |
| E70311 | Autosomal recessive ocular albinism |
| E70318 | Other ocular albinism |
| E70319 | Ocular albinism, unspecified |
| E70320 | Tyrosinase negative oculocutaneous albinism |
| E70321 | Tyrosinase positive oculocutaneous albinism |
| E70328 | Other oculocutaneous albinism |
| E70329 | Oculocutaneous albinism, unspecified |
| E70330 | Chediak-Higashi syndrome |
| E70331 | Hermansky-Pudlak syndrome |
| E70338 | Other albinism with hematologic abnormality |
| E70339 | Albinism with hematologic abnormality, unspecified |
| E7039 | Other specified albinism |
| E7040 | Disorders of histidine metabolism, unspecified |
| E7041 | Histidinemia |
| E7049 | Other disorders of histidine metabolism |
| E705 | Disorders of tryptophan metabolism |
| E7081 | Aromatic L-amino acid decarboxylase deficiency |
| E7089 | Other disorders of aromatic amino-acid metabolism |
| E709 | Disorder of aromatic amino-acid metabolism, unspecified |
| E710 | Maple-syrup-urine disease |
| E71110 | Isovaleric acidemia |
| E71111 | 3-methylglutaconic aciduria |
| E71118 | Other branched-chain organic acidurias |
| E71120 | Methylmalonic acidemia |
| E71121 | Propionic acidemia |
| E71128 | Other disorders of propionate metabolism |
| E7119 | Other disorders of branched-chain amino-acid metabolism |
| E712 | Disorder of branched-chain amino-acid metabolism, unspecified |
| E71310 | Long chain/very long chain acyl CoA dehydrogenase deficiency |
| E71311 | Medium chain acyl CoA dehydrogenase deficiency |
| E71312 | Short chain acyl CoA dehydrogenase deficiency |
| E71313 | Glutaric aciduria type II |
| E71314 | Muscle carnitine palmitoyltransferase deficiency |
| E71318 | Other disorders of fatty-acid oxidation |
| E7132 | Disorders of ketone metabolism |
| E7139 | Other disorders of fatty-acid metabolism |
| E7150 | Peroxisomal disorder, unspecified |
| E71510 | Zellweger syndrome |
| E71511 | Neonatal adrenoleukodystrophy |
| E71518 | Other disorders of peroxisome biogenesis |
| E71520 | Childhood cerebral X-linked adrenoleukodystrophy |
| E71521 | Adolescent X-linked adrenoleukodystrophy |
| E71522 | Adrenomyeloneuropathy |
| E71528 | Other X-linked adrenoleukodystrophy |
| E71529 | X-linked adrenoleukodystrophy, unspecified type |
| E7153 | Other group 2 peroxisomal disorders |
| E71540 | Rhizomelic chondrodysplasia punctata |
| E71541 | Zellweger-like syndrome |
| E71542 | Other group 3 peroxisomal disorders |
| E71548 | Other peroxisomal disorders |
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