DRAFT

ICD-10-CM/PCS MS-DRG v41.0 Definitions Manual

>
Previous Page [Alt-p] Up a level [Alt-u] Next Page [Alt-n]
Appendix C: Principal diagnoses which convert CC/MCC to non-CC
Page 1208 of 1375
PDX Collection 6417 (continued)
E749Disorder of carbohydrate metabolism, unspecified
E7521Fabry (-Anderson) disease
E7522Gaucher disease
E75240Niemann-Pick disease type A
E75241Niemann-Pick disease type B
E75242Niemann-Pick disease type C
E75243Niemann-Pick disease type D
E75248Other Niemann-Pick disease
E75249Niemann-Pick disease, unspecified
E753Sphingolipidosis, unspecified
E755Other lipid storage disorders
E756Lipid storage disorder, unspecified
E770Defects in post-translational modification of lysosomal enzymes
E771Defects in glycoprotein degradation
E778Other disorders of glycoprotein metabolism
E779Disorder of glycoprotein metabolism, unspecified
E7800Pure hypercholesterolemia, unspecified
E7801Familial hypercholesterolemia
E781Pure hyperglyceridemia
E782Mixed hyperlipidemia
E783Hyperchylomicronemia
E7841Elevated Lipoprotein(a)
E7849Other hyperlipidemia
E785Hyperlipidemia, unspecified
E786Lipoprotein deficiency
E7870Disorder of bile acid and cholesterol metabolism, unspecified
E7879Other disorders of bile acid and cholesterol metabolism
E7881Lipoid dermatoarthritis
E7889Other lipoprotein metabolism disorders
E789Disorder of lipoprotein metabolism, unspecified
E8802Plasminogen deficiency
E8809Other disorders of plasma-protein metabolism, not elsewhere classified
E881Lipodystrophy, not elsewhere classified
E882Lipomatosis, not elsewhere classified
E88811Insulin resistance syndrome, Type A
E88818Other insulin resistance
E88819Insulin resistance, unspecified
E8889Other specified metabolic disorders
 
PDX Collection 6418
E7871Barth syndrome
E7872Smith-Lemli-Opitz syndrome
Q872Congenital malformation syndromes predominantly involving limbs
Q873Congenital malformation syndromes involving early overgrowth
Q8740Marfan syndrome, unspecified
Q87410Marfan syndrome with aortic dilation
Q87418Marfan syndrome with other cardiovascular manifestations
Q8742Marfan syndrome with ocular manifestations
Q8743Marfan syndrome with skeletal manifestation
Q875Other congenital malformation syndromes with other skeletal changes
Q8781Alport syndrome
Q8782Arterial tortuosity syndrome
Q8783Bardet-Biedl syndrome
Q8784Laurence-Moon syndrome
Q8785MED13L syndrome
Q8789Other specified congenital malformation syndromes, not elsewhere classified
Q898Other specified congenital malformations
Q992Fragile X chromosome
 
PDX Collection 6419
D8130Adenosine deaminase deficiency, unspecified
D8131Severe combined immunodeficiency due to adenosine deaminase deficiency
D8132Adenosine deaminase 2 deficiency
D8139Other adenosine deaminase deficiency
D815Purine nucleoside phosphorylase [PNP] deficiency
D81810Biotinidase deficiency
D841Defects in the complement system
E7601Hurler's syndrome
E7602Hurler-Scheie syndrome
E7603Scheie's syndrome
E761Mucopolysaccharidosis, type II
E76210Morquio A mucopolysaccharidoses
E76211Morquio B mucopolysaccharidoses
E76219Morquio mucopolysaccharidoses, unspecified
E7622Sanfilippo mucopolysaccharidoses
E7629Other mucopolysaccharidoses
E763Mucopolysaccharidosis, unspecified
E768Other disorders of glucosaminoglycan metabolism
E769Glucosaminoglycan metabolism disorder, unspecified
E791Lesch-Nyhan syndrome
E792Myoadenylate deaminase deficiency
E7981Aicardi-Goutières syndrome
E7982Hereditary xanthinuria
E7989Other specified disorders of purine and pyrimidine metabolism
E799Disorder of purine and pyrimidine metabolism, unspecified
E800Hereditary erythropoietic porphyria
E801Porphyria cutanea tarda
E8020Unspecified porphyria
E8021Acute intermittent (hepatic) porphyria
E8029Other porphyria
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E88810Metabolic syndrome
 
PDX Collection 6420
D8130Adenosine deaminase deficiency, unspecified
D8131Severe combined immunodeficiency due to adenosine deaminase deficiency
D8132Adenosine deaminase 2 deficiency
D8139Other adenosine deaminase deficiency
D815Purine nucleoside phosphorylase [PNP] deficiency
D81810Biotinidase deficiency
D841Defects in the complement system
E7601Hurler's syndrome
E7602Hurler-Scheie syndrome
E7603Scheie's syndrome
E761Mucopolysaccharidosis, type II
E76210Morquio A mucopolysaccharidoses
E76211Morquio B mucopolysaccharidoses
E76219Morquio mucopolysaccharidoses, unspecified
E7622Sanfilippo mucopolysaccharidoses
E7629Other mucopolysaccharidoses
E763Mucopolysaccharidosis, unspecified
E768Other disorders of glucosaminoglycan metabolism
E769Glucosaminoglycan metabolism disorder, unspecified
E791Lesch-Nyhan syndrome
E792Myoadenylate deaminase deficiency
E7981Aicardi-Goutières syndrome
E7982Hereditary xanthinuria
E7989Other specified disorders of purine and pyrimidine metabolism
E799Disorder of purine and pyrimidine metabolism, unspecified
E800Hereditary erythropoietic porphyria
E801Porphyria cutanea tarda
E8020Unspecified porphyria
E8021Acute intermittent (hepatic) porphyria
E8029Other porphyria
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E88810Metabolic syndrome
 
PDX Collection 6421
C880Waldenstrom macroglobulinemia
D472Monoclonal gammopathy
D890Polyclonal hypergammaglobulinemia
D891Cryoglobulinemia
E700Classical phenylketonuria
E701Other hyperphenylalaninemias
E7020Disorder of tyrosine metabolism, unspecified
E7021Tyrosinemia
E7029Other disorders of tyrosine metabolism
E7030Albinism, unspecified
E70310X-linked ocular albinism
E70311Autosomal recessive ocular albinism
E70318Other ocular albinism
E70319Ocular albinism, unspecified
E70320Tyrosinase negative oculocutaneous albinism
E70321Tyrosinase positive oculocutaneous albinism
E70328Other oculocutaneous albinism
E70329Oculocutaneous albinism, unspecified
E70330Chediak-Higashi syndrome
E70331Hermansky-Pudlak syndrome
E70338Other albinism with hematologic abnormality
E70339Albinism with hematologic abnormality, unspecified
E7039Other specified albinism
E7040Disorders of histidine metabolism, unspecified
E7041Histidinemia
E7049Other disorders of histidine metabolism
E705Disorders of tryptophan metabolism
E7081Aromatic L-amino acid decarboxylase deficiency
E7089Other disorders of aromatic amino-acid metabolism
E709Disorder of aromatic amino-acid metabolism, unspecified
E710Maple-syrup-urine disease
E71110Isovaleric acidemia
E711113-methylglutaconic aciduria
E71118Other branched-chain organic acidurias
E71120Methylmalonic acidemia
E71121Propionic acidemia
E71128Other disorders of propionate metabolism
E7119Other disorders of branched-chain amino-acid metabolism
E712Disorder of branched-chain amino-acid metabolism, unspecified
E7130Disorder of fatty-acid metabolism, unspecified
E7200Disorders of amino-acid transport, unspecified
E7201Cystinuria
E7202Hartnup's disease
E7204Cystinosis
E7209Other disorders of amino-acid transport
E7210Disorders of sulfur-bearing amino-acid metabolism, unspecified
E7211Homocystinuria
E7212Methylenetetrahydrofolate reductase deficiency
E7219Other disorders of sulfur-bearing amino-acid metabolism
E7220Disorder of urea cycle metabolism, unspecified
E7221Argininemia
E7222Arginosuccinic aciduria
E7223Citrullinemia
E7229Other disorders of urea cycle metabolism
E723Disorders of lysine and hydroxylysine metabolism
E724Disorders of ornithine metabolism
E7250Disorder of glycine metabolism, unspecified
E7251Non-ketotic hyperglycinemia
E7252Trimethylaminuria
E7253Primary hyperoxaluria
E7259Other disorders of glycine metabolism
E7281Disorders of gamma aminobutyric acid metabolism
E7289Other specified disorders of amino-acid metabolism
E729Disorder of amino-acid metabolism, unspecified
E730Congenital lactase deficiency
E731Secondary lactase deficiency
E738Other lactose intolerance
E739Lactose intolerance, unspecified
E7400Glycogen storage disease, unspecified
E7401von Gierke disease
E7402Pompe disease
E7403Cori disease
E7404McArdle disease
E7405Lysosome-associated membrane protein 2 [LAMP2] deficiency
E7409Other glycogen storage disease
E7410Disorder of fructose metabolism, unspecified
E7411Essential fructosuria
E7412Hereditary fructose intolerance
E7419Other disorders of fructose metabolism
E7420Disorders of galactose metabolism, unspecified
E7421Galactosemia
E7429Other disorders of galactose metabolism
E7431Sucrase-isomaltase deficiency
E7439Other disorders of intestinal carbohydrate absorption
E744Disorders of pyruvate metabolism and gluconeogenesis
E74810Glucose transporter protein type 1 deficiency
E74818Other disorders of glucose transport
E74819Disorders of glucose transport, unspecified
E7489Other specified disorders of carbohydrate metabolism
E749Disorder of carbohydrate metabolism, unspecified
E7521Fabry (-Anderson) disease
E7522Gaucher disease
E75240Niemann-Pick disease type A
E75241Niemann-Pick disease type B
E75242Niemann-Pick disease type C
E75243Niemann-Pick disease type D
E75248Other Niemann-Pick disease
E75249Niemann-Pick disease, unspecified
E753Sphingolipidosis, unspecified
E755Other lipid storage disorders
E756Lipid storage disorder, unspecified
E770Defects in post-translational modification of lysosomal enzymes
E771Defects in glycoprotein degradation
E778Other disorders of glycoprotein metabolism
E779Disorder of glycoprotein metabolism, unspecified
E7800Pure hypercholesterolemia, unspecified
E7801Familial hypercholesterolemia
E781Pure hyperglyceridemia
E782Mixed hyperlipidemia
E783Hyperchylomicronemia
E7841Elevated Lipoprotein(a)
E7849Other hyperlipidemia
E785Hyperlipidemia, unspecified
E786Lipoprotein deficiency
E7870Disorder of bile acid and cholesterol metabolism, unspecified
E7879Other disorders of bile acid and cholesterol metabolism
E7881Lipoid dermatoarthritis
E7889Other lipoprotein metabolism disorders
E789Disorder of lipoprotein metabolism, unspecified
E8802Plasminogen deficiency
E8809Other disorders of plasma-protein metabolism, not elsewhere classified
E881Lipodystrophy, not elsewhere classified
E882Lipomatosis, not elsewhere classified
E88811Insulin resistance syndrome, Type A
E88818Other insulin resistance
E88819Insulin resistance, unspecified
E8889Other specified metabolic disorders
 
PDX Collection 6422
C880Waldenstrom macroglobulinemia
D472Monoclonal gammopathy
D890Polyclonal hypergammaglobulinemia
D891Cryoglobulinemia
E700Classical phenylketonuria
E701Other hyperphenylalaninemias
E7020Disorder of tyrosine metabolism, unspecified
E7021Tyrosinemia
E7029Other disorders of tyrosine metabolism
E7030Albinism, unspecified
E70310X-linked ocular albinism
E70311Autosomal recessive ocular albinism
E70318Other ocular albinism
E70319Ocular albinism, unspecified
E70320Tyrosinase negative oculocutaneous albinism
E70321Tyrosinase positive oculocutaneous albinism
E70328Other oculocutaneous albinism
E70329Oculocutaneous albinism, unspecified
E70330Chediak-Higashi syndrome
E70331Hermansky-Pudlak syndrome
E70338Other albinism with hematologic abnormality
E70339Albinism with hematologic abnormality, unspecified
E7039Other specified albinism
E7040Disorders of histidine metabolism, unspecified
E7041Histidinemia
E7049Other disorders of histidine metabolism
E705Disorders of tryptophan metabolism
E7081Aromatic L-amino acid decarboxylase deficiency
E7089Other disorders of aromatic amino-acid metabolism
E709Disorder of aromatic amino-acid metabolism, unspecified
E710Maple-syrup-urine disease
E71110Isovaleric acidemia
E711113-methylglutaconic aciduria
E71118Other branched-chain organic acidurias
E71120Methylmalonic acidemia
E71121Propionic acidemia
E71128Other disorders of propionate metabolism
E7119Other disorders of branched-chain amino-acid metabolism
E712Disorder of branched-chain amino-acid metabolism, unspecified
E7130Disorder of fatty-acid metabolism, unspecified
E7200Disorders of amino-acid transport, unspecified
E7201Cystinuria
E7202Hartnup's disease
E7204Cystinosis
E7209Other disorders of amino-acid transport
E7210Disorders of sulfur-bearing amino-acid metabolism, unspecified
E7211Homocystinuria
E7212Methylenetetrahydrofolate reductase deficiency
E7219Other disorders of sulfur-bearing amino-acid metabolism
E7220Disorder of urea cycle metabolism, unspecified
E7221Argininemia
E7222Arginosuccinic aciduria
E7223Citrullinemia
E7229Other disorders of urea cycle metabolism
E723Disorders of lysine and hydroxylysine metabolism
E724Disorders of ornithine metabolism
E7250Disorder of glycine metabolism, unspecified
E7251Non-ketotic hyperglycinemia
E7252Trimethylaminuria
E7253Primary hyperoxaluria
E7259Other disorders of glycine metabolism
E7281Disorders of gamma aminobutyric acid metabolism
E7289Other specified disorders of amino-acid metabolism
E729Disorder of amino-acid metabolism, unspecified
E730Congenital lactase deficiency
E731Secondary lactase deficiency
E738Other lactose intolerance
E739Lactose intolerance, unspecified
E7400Glycogen storage disease, unspecified
E7401von Gierke disease
E7402Pompe disease
E7403Cori disease
E7404McArdle disease
E7405Lysosome-associated membrane protein 2 [LAMP2] deficiency
E7409Other glycogen storage disease
E7410Disorder of fructose metabolism, unspecified
E7411Essential fructosuria
E7412Hereditary fructose intolerance
E7419Other disorders of fructose metabolism
E7420Disorders of galactose metabolism, unspecified
E7421Galactosemia
E7429Other disorders of galactose metabolism
E7431Sucrase-isomaltase deficiency
E7439Other disorders of intestinal carbohydrate absorption
E744Disorders of pyruvate metabolism and gluconeogenesis
E74810Glucose transporter protein type 1 deficiency
E74818Other disorders of glucose transport
E74819Disorders of glucose transport, unspecified
E7489Other specified disorders of carbohydrate metabolism
E749Disorder of carbohydrate metabolism, unspecified
E7521Fabry (-Anderson) disease
E7522Gaucher disease
E75240Niemann-Pick disease type A
E75241Niemann-Pick disease type B
E75242Niemann-Pick disease type C
E75243Niemann-Pick disease type D
E75248Other Niemann-Pick disease
E75249Niemann-Pick disease, unspecified
E753Sphingolipidosis, unspecified
E755Other lipid storage disorders
E756Lipid storage disorder, unspecified
E770Defects in post-translational modification of lysosomal enzymes
E771Defects in glycoprotein degradation
E778Other disorders of glycoprotein metabolism
E779Disorder of glycoprotein metabolism, unspecified
E7800Pure hypercholesterolemia, unspecified
E7801Familial hypercholesterolemia
E781Pure hyperglyceridemia
E782Mixed hyperlipidemia
E783Hyperchylomicronemia
E7841Elevated Lipoprotein(a)
E7849Other hyperlipidemia
E785Hyperlipidemia, unspecified
E786Lipoprotein deficiency
E7870Disorder of bile acid and cholesterol metabolism, unspecified
E7879Other disorders of bile acid and cholesterol metabolism
E7881Lipoid dermatoarthritis
E7889Other lipoprotein metabolism disorders
E789Disorder of lipoprotein metabolism, unspecified
E8802Plasminogen deficiency
E8809Other disorders of plasma-protein metabolism, not elsewhere classified
E881Lipodystrophy, not elsewhere classified
E882Lipomatosis, not elsewhere classified
E88811Insulin resistance syndrome, Type A
E88818Other insulin resistance
E88819Insulin resistance, unspecified
E8889Other specified metabolic disorders
 
PDX Collection 6423
K634Enteroptosis
K638211Small intestinal bacterial overgrowth, hydrogen-subtype
K638212Small intestinal bacterial overgrowth, hydrogen sulfide-subtype
K638219Small intestinal bacterial overgrowth, unspecified
K63822Small intestinal fungal overgrowth
K63829Intestinal methanogen overgrowth, unspecified
K6389Other specified diseases of intestine
K639Disease of intestine, unspecified
K650Generalized (acute) peritonitis
K651Peritoneal abscess
K652Spontaneous bacterial peritonitis
K653Choleperitonitis
K654Sclerosing mesenteritis
K658Other peritonitis
K659Peritonitis, unspecified
K67Disorders of peritoneum in infectious diseases classified elsewhere
K6819Other retroperitoneal abscess
K682Retroperitoneal fibrosis
K683Retroperitoneal hematoma
K689Other disorders of retroperitoneum
K9289Other specified diseases of the digestive system



Centers for Medicare & Medicaid Services, 7500 Security Boulevard Baltimore, MD 21244
01 Mar 2023 06:12:40
CMS, code-revision=344, description-revision=1357