DRAFT

ICD-10-CM/PCS MS-DRG v41.0 Definitions Manual

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Appendix C: Principal diagnoses which convert CC/MCC to non-CC
Page 1209 of 1375
PDX Collection 6423 (continued)
K929Disease of digestive system, unspecified
R1113Vomiting of fecal matter
 
PDX Collection 6424
D8130Adenosine deaminase deficiency, unspecified
D8131Severe combined immunodeficiency due to adenosine deaminase deficiency
D8132Adenosine deaminase 2 deficiency
D8139Other adenosine deaminase deficiency
D815Purine nucleoside phosphorylase [PNP] deficiency
D81810Biotinidase deficiency
D841Defects in the complement system
E7601Hurler's syndrome
E7602Hurler-Scheie syndrome
E7603Scheie's syndrome
E761Mucopolysaccharidosis, type II
E76210Morquio A mucopolysaccharidoses
E76211Morquio B mucopolysaccharidoses
E76219Morquio mucopolysaccharidoses, unspecified
E7622Sanfilippo mucopolysaccharidoses
E7629Other mucopolysaccharidoses
E763Mucopolysaccharidosis, unspecified
E768Other disorders of glucosaminoglycan metabolism
E769Glucosaminoglycan metabolism disorder, unspecified
E791Lesch-Nyhan syndrome
E792Myoadenylate deaminase deficiency
E7981Aicardi-Goutières syndrome
E7982Hereditary xanthinuria
E7989Other specified disorders of purine and pyrimidine metabolism
E799Disorder of purine and pyrimidine metabolism, unspecified
E800Hereditary erythropoietic porphyria
E801Porphyria cutanea tarda
E8020Unspecified porphyria
E8021Acute intermittent (hepatic) porphyria
E8029Other porphyria
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E88810Metabolic syndrome
 
PDX Collection 6425
E7871Barth syndrome
E7872Smith-Lemli-Opitz syndrome
P2930Pulmonary hypertension of newborn
P2938Other persistent fetal circulation
Q251Coarctation of aorta
Q2521Interruption of aortic arch
Q2529Other atresia of aorta
Q253Supravalvular aortic stenosis
Q2730Arteriovenous malformation, site unspecified
Q274Congenital phlebectasia
Q280Arteriovenous malformation of precerebral vessels
Q281Other malformations of precerebral vessels
Q288Other specified congenital malformations of circulatory system
Q289Congenital malformation of circulatory system, unspecified
Q8711Prader-Willi syndrome
Q8719Other congenital malformation syndromes predominantly associated with short stature
Q872Congenital malformation syndromes predominantly involving limbs
Q873Congenital malformation syndromes involving early overgrowth
Q8740Marfan syndrome, unspecified
Q87410Marfan syndrome with aortic dilation
Q87418Marfan syndrome with other cardiovascular manifestations
Q8742Marfan syndrome with ocular manifestations
Q8743Marfan syndrome with skeletal manifestation
Q875Other congenital malformation syndromes with other skeletal changes
Q8781Alport syndrome
Q8782Arterial tortuosity syndrome
Q8783Bardet-Biedl syndrome
Q8784Laurence-Moon syndrome
Q8785MED13L syndrome
Q8789Other specified congenital malformation syndromes, not elsewhere classified
Q897Multiple congenital malformations, not elsewhere classified
Q898Other specified congenital malformations
Q992Fragile X chromosome
 
PDX Collection 6426
A150Tuberculosis of lung
A154Tuberculosis of intrathoracic lymph nodes
A155Tuberculosis of larynx, trachea and bronchus
A156Tuberculous pleurisy
A158Other respiratory tuberculosis
A159Respiratory tuberculosis unspecified
A179Tuberculosis of nervous system, unspecified
A1882Tuberculosis of other endocrine glands
A1884Tuberculosis of heart
A1889Tuberculosis of other sites
A212Pulmonary tularemia
A221Pulmonary anthrax
A310Pulmonary mycobacterial infection
A3701Whooping cough due to Bordetella pertussis with pneumonia
A3711Whooping cough due to Bordetella parapertussis with pneumonia
A3781Whooping cough due to other Bordetella species with pneumonia
A3791Whooping cough, unspecified species with pneumonia
A420Pulmonary actinomycosis
A430Pulmonary nocardiosis
A481Legionnaires' disease
B250Cytomegaloviral pneumonitis
B390Acute pulmonary histoplasmosis capsulati
B391Chronic pulmonary histoplasmosis capsulati
B392Pulmonary histoplasmosis capsulati, unspecified
B440Invasive pulmonary aspergillosis
B583Pulmonary toxoplasmosis
B59Pneumocystosis
B671Echinococcus granulosus infection of lung
J09X1Influenza due to identified novel influenza A virus with pneumonia
J09X2Influenza due to identified novel influenza A virus with other respiratory manifestations
J1000Influenza due to other identified influenza virus with unspecified type of pneumonia
J1001Influenza due to other identified influenza virus with the same other identified influenza virus pneumonia
J1008Influenza due to other identified influenza virus with other specified pneumonia
J101Influenza due to other identified influenza virus with other respiratory manifestations
J1100Influenza due to unidentified influenza virus with unspecified type of pneumonia
J1108Influenza due to unidentified influenza virus with specified pneumonia
J111Influenza due to unidentified influenza virus with other respiratory manifestations
J120Adenoviral pneumonia
J121Respiratory syncytial virus pneumonia
J122Parainfluenza virus pneumonia
J123Human metapneumovirus pneumonia
J1289Other viral pneumonia
J129Viral pneumonia, unspecified
J13Pneumonia due to Streptococcus pneumoniae
J14Pneumonia due to Hemophilus influenzae
J150Pneumonia due to Klebsiella pneumoniae
J151Pneumonia due to Pseudomonas
J1520Pneumonia due to staphylococcus, unspecified
J15211Pneumonia due to Methicillin susceptible Staphylococcus aureus
J15212Pneumonia due to Methicillin resistant Staphylococcus aureus
J1529Pneumonia due to other staphylococcus
J153Pneumonia due to streptococcus, group B
J154Pneumonia due to other streptococci
J155Pneumonia due to Escherichia coli
J1561Pneumonia due to Acinetobacter baumannii
J1569Pneumonia due to other Gram-negative bacteria
J157Pneumonia due to Mycoplasma pneumoniae
J158Pneumonia due to other specified bacteria
J159Unspecified bacterial pneumonia
J160Chlamydial pneumonia
J168Pneumonia due to other specified infectious organisms
J180Bronchopneumonia, unspecified organism
J181Lobar pneumonia, unspecified organism
J188Other pneumonia, unspecified organism
J189Pneumonia, unspecified organism
J22Unspecified acute lower respiratory infection
J4481Bronchiolitis obliterans and bronchiolitis obliterans syndrome
J449Chronic obstructive pulmonary disease, unspecified
J470Bronchiectasis with acute lower respiratory infection
J471Bronchiectasis with (acute) exacerbation
J479Bronchiectasis, uncomplicated
J60Coalworker's pneumoconiosis
J61Pneumoconiosis due to asbestos and other mineral fibers
J620Pneumoconiosis due to talc dust
J628Pneumoconiosis due to other dust containing silica
J630Aluminosis (of lung)
J631Bauxite fibrosis (of lung)
J632Berylliosis
J633Graphite fibrosis (of lung)
J634Siderosis
J635Stannosis
J636Pneumoconiosis due to other specified inorganic dusts
J64Unspecified pneumoconiosis
J65Pneumoconiosis associated with tuberculosis
J660Byssinosis
J661Flax-dressers' disease
J662Cannabinosis
J668Airway disease due to other specific organic dusts
J670Farmer's lung
J671Bagassosis
J672Bird fancier's lung
J673Suberosis
J674Maltworker's lung
J675Mushroom-worker's lung
J676Maple-bark-stripper's lung
J677Air conditioner and humidifier lung
J678Hypersensitivity pneumonitis due to other organic dusts
J679Hypersensitivity pneumonitis due to unspecified organic dust
J680Bronchitis and pneumonitis due to chemicals, gases, fumes and vapors
J681Pulmonary edema due to chemicals, gases, fumes and vapors
J682Upper respiratory inflammation due to chemicals, gases, fumes and vapors, not elsewhere classified
J683Other acute and subacute respiratory conditions due to chemicals, gases, fumes and vapors
J684Chronic respiratory conditions due to chemicals, gases, fumes and vapors
J688Other respiratory conditions due to chemicals, gases, fumes and vapors
J689Unspecified respiratory condition due to chemicals, gases, fumes and vapors
J690Pneumonitis due to inhalation of food and vomit
J691Pneumonitis due to inhalation of oils and essences
J698Pneumonitis due to inhalation of other solids and liquids
J700Acute pulmonary manifestations due to radiation
J701Chronic and other pulmonary manifestations due to radiation
J702Acute drug-induced interstitial lung disorders
J703Chronic drug-induced interstitial lung disorders
J704Drug-induced interstitial lung disorders, unspecified
J708Respiratory conditions due to other specified external agents
J709Respiratory conditions due to unspecified external agent
J984Other disorders of lung
J988Other specified respiratory disorders
J989Respiratory disorder, unspecified
N80B1Endometriosis of pleura
N80B2Endometriosis of lung
N80B31Superficial endometriosis of diaphragm
N80B32Deep endometriosis of diaphragm
N80B39Endometriosis of diaphragm, unspecified depth
Q334Congenital bronchiectasis
R911Solitary pulmonary nodule
 
PDX Collection 6427
E8419Cystic fibrosis with other intestinal manifestations
K900Celiac disease
K901Tropical sprue
K902Blind loop syndrome, not elsewhere classified
K903Pancreatic steatorrhea
K9041Non-celiac gluten sensitivity
K9049Malabsorption due to intolerance, not elsewhere classified
K90821Short bowel syndrome with colon in continuity
K90822Short bowel syndrome without colon in continuity
K90829Short bowel syndrome, unspecified
K9083Intestinal failure
K9089Other intestinal malabsorption
K909Intestinal malabsorption, unspecified
K912Postsurgical malabsorption, not elsewhere classified
 
PDX Collection 6428
E7871Barth syndrome
E7872Smith-Lemli-Opitz syndrome
P2930Pulmonary hypertension of newborn
P2938Other persistent fetal circulation
Q251Coarctation of aorta
Q2521Interruption of aortic arch
Q2529Other atresia of aorta
Q253Supravalvular aortic stenosis
Q2730Arteriovenous malformation, site unspecified
Q274Congenital phlebectasia
Q280Arteriovenous malformation of precerebral vessels
Q281Other malformations of precerebral vessels
Q288Other specified congenital malformations of circulatory system
Q289Congenital malformation of circulatory system, unspecified
Q8711Prader-Willi syndrome
Q8719Other congenital malformation syndromes predominantly associated with short stature
Q872Congenital malformation syndromes predominantly involving limbs
Q873Congenital malformation syndromes involving early overgrowth
Q8740Marfan syndrome, unspecified
Q87410Marfan syndrome with aortic dilation
Q87418Marfan syndrome with other cardiovascular manifestations
Q8742Marfan syndrome with ocular manifestations
Q8743Marfan syndrome with skeletal manifestation
Q875Other congenital malformation syndromes with other skeletal changes
Q8781Alport syndrome
Q8782Arterial tortuosity syndrome
Q8783Bardet-Biedl syndrome
Q8784Laurence-Moon syndrome
Q8785MED13L syndrome
Q8789Other specified congenital malformation syndromes, not elsewhere classified
Q897Multiple congenital malformations, not elsewhere classified
Q898Other specified congenital malformations
Q992Fragile X chromosome
 
PDX Collection 6429
C880Waldenstrom macroglobulinemia
D472Monoclonal gammopathy
D890Polyclonal hypergammaglobulinemia
D891Cryoglobulinemia
E700Classical phenylketonuria
E701Other hyperphenylalaninemias
E7020Disorder of tyrosine metabolism, unspecified
E7021Tyrosinemia
E7029Other disorders of tyrosine metabolism
E7030Albinism, unspecified
E70310X-linked ocular albinism
E70311Autosomal recessive ocular albinism
E70318Other ocular albinism
E70319Ocular albinism, unspecified
E70320Tyrosinase negative oculocutaneous albinism
E70321Tyrosinase positive oculocutaneous albinism
E70328Other oculocutaneous albinism
E70329Oculocutaneous albinism, unspecified
E70330Chediak-Higashi syndrome
E70331Hermansky-Pudlak syndrome
E70338Other albinism with hematologic abnormality
E70339Albinism with hematologic abnormality, unspecified
E7039Other specified albinism
E7040Disorders of histidine metabolism, unspecified
E7041Histidinemia
E7049Other disorders of histidine metabolism
E705Disorders of tryptophan metabolism
E7081Aromatic L-amino acid decarboxylase deficiency
E7089Other disorders of aromatic amino-acid metabolism
E709Disorder of aromatic amino-acid metabolism, unspecified
E710Maple-syrup-urine disease
E71110Isovaleric acidemia
E711113-methylglutaconic aciduria
E71118Other branched-chain organic acidurias
E71120Methylmalonic acidemia
E71121Propionic acidemia
E71128Other disorders of propionate metabolism
E7119Other disorders of branched-chain amino-acid metabolism
E712Disorder of branched-chain amino-acid metabolism, unspecified
E7130Disorder of fatty-acid metabolism, unspecified
E7200Disorders of amino-acid transport, unspecified
E7201Cystinuria
E7202Hartnup's disease
E7204Cystinosis
E7209Other disorders of amino-acid transport
E7210Disorders of sulfur-bearing amino-acid metabolism, unspecified
E7211Homocystinuria
E7212Methylenetetrahydrofolate reductase deficiency
E7219Other disorders of sulfur-bearing amino-acid metabolism
E7220Disorder of urea cycle metabolism, unspecified
E7221Argininemia
E7222Arginosuccinic aciduria
E7223Citrullinemia
E7229Other disorders of urea cycle metabolism
E723Disorders of lysine and hydroxylysine metabolism
E724Disorders of ornithine metabolism
E7250Disorder of glycine metabolism, unspecified
E7251Non-ketotic hyperglycinemia
E7252Trimethylaminuria
E7253Primary hyperoxaluria
E7259Other disorders of glycine metabolism
E7281Disorders of gamma aminobutyric acid metabolism
E7289Other specified disorders of amino-acid metabolism
E729Disorder of amino-acid metabolism, unspecified
E730Congenital lactase deficiency
E731Secondary lactase deficiency
E738Other lactose intolerance
E739Lactose intolerance, unspecified
E7400Glycogen storage disease, unspecified
E7401von Gierke disease
E7402Pompe disease
E7403Cori disease
E7404McArdle disease
E7405Lysosome-associated membrane protein 2 [LAMP2] deficiency
E7409Other glycogen storage disease
E7410Disorder of fructose metabolism, unspecified
E7411Essential fructosuria
E7412Hereditary fructose intolerance
E7419Other disorders of fructose metabolism
E7420Disorders of galactose metabolism, unspecified
E7421Galactosemia
E7429Other disorders of galactose metabolism
E7431Sucrase-isomaltase deficiency
E7439Other disorders of intestinal carbohydrate absorption
E744Disorders of pyruvate metabolism and gluconeogenesis
E74810Glucose transporter protein type 1 deficiency
E74818Other disorders of glucose transport
E74819Disorders of glucose transport, unspecified
E7489Other specified disorders of carbohydrate metabolism
E749Disorder of carbohydrate metabolism, unspecified
E7521Fabry (-Anderson) disease
E7522Gaucher disease
E75240Niemann-Pick disease type A
E75241Niemann-Pick disease type B
E75242Niemann-Pick disease type C
E75243Niemann-Pick disease type D
E75248Other Niemann-Pick disease
E75249Niemann-Pick disease, unspecified
E753Sphingolipidosis, unspecified
E755Other lipid storage disorders
E756Lipid storage disorder, unspecified
E770Defects in post-translational modification of lysosomal enzymes
E771Defects in glycoprotein degradation
E778Other disorders of glycoprotein metabolism
E779Disorder of glycoprotein metabolism, unspecified
E7800Pure hypercholesterolemia, unspecified
E7801Familial hypercholesterolemia
E781Pure hyperglyceridemia
E782Mixed hyperlipidemia
E783Hyperchylomicronemia
E7841Elevated Lipoprotein(a)
E7849Other hyperlipidemia
E785Hyperlipidemia, unspecified
E786Lipoprotein deficiency
E7870Disorder of bile acid and cholesterol metabolism, unspecified
E7879Other disorders of bile acid and cholesterol metabolism
E7881Lipoid dermatoarthritis
E7889Other lipoprotein metabolism disorders
E789Disorder of lipoprotein metabolism, unspecified
E8802Plasminogen deficiency
E8809Other disorders of plasma-protein metabolism, not elsewhere classified
E881Lipodystrophy, not elsewhere classified
E882Lipomatosis, not elsewhere classified
E88811Insulin resistance syndrome, Type A
E88818Other insulin resistance
E88819Insulin resistance, unspecified
E8889Other specified metabolic disorders
 
PDX Collection 6430
C880Waldenstrom macroglobulinemia
D472Monoclonal gammopathy
D890Polyclonal hypergammaglobulinemia
D891Cryoglobulinemia
E700Classical phenylketonuria
E701Other hyperphenylalaninemias
E7020Disorder of tyrosine metabolism, unspecified
E7021Tyrosinemia
E7029Other disorders of tyrosine metabolism
E7030Albinism, unspecified
E70310X-linked ocular albinism
E70311Autosomal recessive ocular albinism
E70318Other ocular albinism
E70319Ocular albinism, unspecified
E70320Tyrosinase negative oculocutaneous albinism
E70321Tyrosinase positive oculocutaneous albinism
E70328Other oculocutaneous albinism
E70329Oculocutaneous albinism, unspecified
E70330Chediak-Higashi syndrome
E70331Hermansky-Pudlak syndrome
E70338Other albinism with hematologic abnormality
E70339Albinism with hematologic abnormality, unspecified
E7039Other specified albinism
E7040Disorders of histidine metabolism, unspecified
E7041Histidinemia
E7049Other disorders of histidine metabolism
E705Disorders of tryptophan metabolism
E7081Aromatic L-amino acid decarboxylase deficiency
E7089Other disorders of aromatic amino-acid metabolism
E709Disorder of aromatic amino-acid metabolism, unspecified
E710Maple-syrup-urine disease
E71110Isovaleric acidemia



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